Argininosuccinate Lyase (ASL) anticorps (HRP)

Détails pour le produit réf. ABIN1712111, Fournisseur: Connectez-vous pour afficher
Antigène
  • BA4879
  • PSPTO0125
  • ASAL
  • 2510006M18Rik
  • zgc:63532
  • ASL
  • CRYD2
  • argininosuccinate lyase
  • argH-2
  • argH
  • SPBC1539.03c
  • arg7
  • CNC04420
  • STHERM_c13370
  • ASL
  • Asl
  • asl
  • ASL2
Alternatives
anti-Humain Argininosuccinate Lyase anticorps pour Immunofluorescence (fixed cells)
Reactivité
Humain, Souris, Rat (Rattus)
55
33
27
6
6
6
6
6
5
4
3
3
3
3
3
3
2
Hôte
Lapin
44
11
Clonalité
Polyclonal
Conjugué
HRP
2
2
1
1
1
1
1
1
1
1
1
1
1
1
1
1
Application
Immunohistochemistry (Paraffin-embedded Sections) (IHC (p)), Western Blotting (WB)
36
13
11
8
7
7
6
4
2
2
1
1
1
1
Options
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Immunogène KLH conjugated synthetic peptide derived from human ASL/Argininosuccinate Lyase
Isotype IgG
Purification Purified by Protein A.
Autre désignation Asl/Argininosuccinate Lyase (ASL Antibody Extrait)
Sujet

ASL is a member of the lyase 1 family of proteins and is predominantly expressed in the liver. Localizing to the cytoplasm and existing as a homotetramer, ASL catalyzes the hydrolytic cleavage of argininosuccinic acid (ASA) to fumarate and arginine, an essential step of the urea cycle which is crucial for the detoxification of ammonia. This reaction is also involved in the biosynthesis of arginine. In addition, ASL shares high sequence homology with the avian and reptilian eye lens protein, d-crystallin. Mutations in the gene encoding ASL leads to an accumulation of ASA in body fluids and results in Arginosuc-cinic aciduria (ASAuria), an autosomal recessive disorder that is characterized by hyperammonemia, liver enlargement, convulsions, physical and mental retardation, episodic unconsciousness and dry and brittle hair showing trich-orrhexis nodosa (weak points or nodes in the hair shaft).

Synonyms: Argininosuccinase, Argininosuccinate lyase, Arginosuccinase, ARLY_HUMAN, ASAL, ASL, EC 4.3.2.1.

ID gène 435
Pathways Response to Growth Hormone Stimulus
Indications d'application WB 1:100-1000
IHC-P 1:100-500
Restrictions For Research Use only
Format Liquid
Concentration 1 μg/μL
Buffer Aqueous buffered solution containing 1 % BSA, 50 % glycerol and 0.09 % Gentamicin.
Agent conservateur Gentamicin sulfate
Précaution d'utilisation This product contains Gentamicin sulfate: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Conseil sur la manipulation Do NOT add Sodium Azide! Use of Sodium Azide will inhibit enzyme activity of horseradish peroxidase.
Stock 4 °C
Stockage commentaire Store at 4°C
Date de péremption 12 months