Galactosamine (N-Acetyl)-6-Sulfate Sulfatase (GALNS) anticorps (HRP)

Détails pour le produit réf. ABIN1712305, Fournisseur: Connectez-vous pour afficher
Antigène
  • GALNAC6S
  • GAS
  • GalN6S
  • MPS4A
  • mFLJ00319
  • N-acetylgalactosamine-6-sulfatase
  • galactosamine (N-acetyl)-6-sulfate sulfatase
  • Plabr_0892
  • Plabr_1680
  • Plabr_2744
  • Plabr_3133
  • Plabr_3297
  • Plabr_3918
  • Plabr_3935
  • Plabr_4057
  • Plabr_4157
  • Plabr_4160
  • Plabr_4308
  • Plabr_4647
  • Celly_0425
  • Halhy_0527
  • Halhy_2233
  • Halhy_4972
  • GALNS
  • Galns
Alternatives
anti-Souris Galactosamine (N-Acetyl)-6-Sulfate Sulfatase anticorps pour Immunofluorescence (fixed cells)
Reactivité
Humain, Souris, Rat (Rattus)
90
29
27
Hôte
Lapin
75
16
3
Clonalité
Polyclonal
Conjugué
HRP
7
7
6
3
3
3
1
1
1
1
1
1
1
1
1
1
1
Application
Immunohistochemistry (Paraffin-embedded Sections) (IHC (p)), Western Blotting (WB)
69
36
32
22
18
17
13
12
5
2
1
1
1
Options
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Immunogène KLH conjugated synthetic peptide derived from human GALNS
Isotype IgG
Purification Purified by Protein A.
Autre désignation Galns (GALNS Antibody Extrait)
Sujet

Chondroitinase is a 522 amino acid protein that localizes to the lysosome and functions as an exohydrolase that is essential for the degradation of glycosaminoglycans, keratan sulfate and chondroitin 6-sulfate. Using calcium as a cofactor, Chondroitinase, which exists as a disulfide linked oligomer, catalyzes the hydrolysis of the 6-sulfate group on target substrates. Defects in the gene encoding Chondroitinase are the cause of mucopolysaccharidosis type 4A (MPS4A), an autosomal recessive lysosomal storage disease that is characterized by the intracellular accumulation of keratan sulfate and chondroitin-6-sulfate and is associated with dental anomalies, short stature and, in some cases, death in the second or third decade of life.

Synonyms: Chondroitinase, Chondroitinsulfatase, FLJ00319, FLJ17434, FLJ42844, FLJ98217, Galactosamine N acetyl 6 sulfate sulfatase, Galactose 6 sulfate sulfatase, GALNAC6S, GalNAc6S sulfatase, GAS, mFLJ00319, MPS4A, N acetylgalactosamine 6 sulfatase, N acetylgalactosamine 6 sulfate sulfatase, GALNS_HUMAN.

ID gène 2588
Domaine de recherche Proteolysis / Ubiquitin, Extracellular Matrix, Organelles
Pathways Glycosaminoglycan Metabolic Process
Indications d'application WB 1:100-1000
IHC-P 1:100-500
Restrictions For Research Use only
Format Liquid
Concentration 1 μg/μL
Buffer Aqueous buffered solution containing 1 % BSA, 50 % glycerol and 0.09 % Gentamicin.
Agent conservateur Gentamicin sulfate
Précaution d'utilisation This product contains Gentamicin sulfate: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Conseil sur la manipulation Do NOT add Sodium Azide! Use of Sodium Azide will inhibit enzyme activity of horseradish peroxidase.
Stock 4 °C
Stockage commentaire Store at 4°C
Date de péremption 12 months