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HPS3 anticorps (C-Term)

HPS3 Reactivité: Humain WB Hôte: Chèvre Polyclonal unconjugated
N° du produit ABIN374450
  • Antigène Voir toutes HPS3 Anticorps
    HPS3 (Hermansky-Pudlak Syndrome 3 (HPS3))
    Épitope
    • 8
    • 8
    • 6
    • 2
    • 2
    • 1
    • 1
    C-Term
    Reactivité
    • 23
    • 3
    • 3
    • 2
    • 2
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    Humain
    Hôte
    • 21
    • 1
    • 1
    Chèvre
    Clonalité
    • 23
    Polyclonal
    Conjugué
    • 13
    • 2
    • 2
    • 2
    • 2
    • 2
    Cet anticorp HPS3 est non-conjugé
    Application
    • 23
    • 15
    • 4
    • 2
    • 2
    • 2
    Western Blotting (WB)
    Séquence
    PYLLYCSRKK PLT
    Specificité
    This antibody recognizes HPS3/Cocoa
    Réactivité croisée (Details)
    Species reactivity (tested):Human.
    Purification
    Ammonium Sulphate Precipitation followed by antigen Affinity Chromatography using the immunizing peptide.
    Immunogène
    Peptide from the C Terminus of the protein sequence according to NP_115759
    Top Product
    Discover our top product HPS3 Anticorps primaire
  • Indications d'application
    Peptide ELISA: > 1/32,000. Western Blot: 1-3 μg/mL. Detects a band of Approx 110 kDa in A431 cell lysate(Predicted Molecular Weight: 114 kDa).
    Other applications not tested.
    Optimal dilutions are dependent on conditions and should be determined by the user.
    Restrictions
    For Research Use only
  • Concentration
    0.5 mg/mL
    Buffer
    Tris saline, pH 7.3 containing 0.02 % Sodium Azide as preservative and 0.5 % BSA as stabilizer.
    Agent conservateur
    Sodium azide
    Précaution d'utilisation
    This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    Conseil sur la manipulation
    Avoid repeated freezing and thawing.
    Stock
    -20 °C
    Stockage commentaire
    Store the antibody (in aliquots) at -20 °C.
  • Antigène
    HPS3 (Hermansky-Pudlak Syndrome 3 (HPS3))
    Autre désignation
    HPS3 (HPS3 Produits)
    Synonymes
    anticorps SUTAL, anticorps HPS3, anticorps coa, anticorps HPS3, biogenesis of lysosomal organelles complex 2 subunit 1, anticorps HPS3, biogenesis of lysosomal organelles complex 2 subunit 1 L homeolog, anticorps Hermansky-Pudlak syndrome 3, anticorps HPS3, anticorps hps3.L, anticorps Hps3
    Sujet
    HPS3 is involved in early stages of melanosome biogenesis and maturation. Defects in HPS3 are the cause of the cocoa (coa) mutant, and of Hermansky-Pudlak syndrome type 3 (HPS3). HPS3 is an autosomal recessive disorder, characterized by oculocutaneous albinism, bleeding due to platelet storage pool deficiency, and lysosomal storage defects. This syndrome results from defects of diverse cytoplasmic organelles including melanosomes, platelet dense granules and lysosomes. Ceroid storage in the lungs is associated with pulmonary fibrosis, a common cause of premature death in individuals with HPS.Synonyms: Hermansky-Pudlak syndrome 3
    ID gène
    84343
    NCBI Accession
    NP_115759
    UniProt
    Q969F9
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