DBT Kits ELISA
The branched-chain alpha-keto acid dehydrogenase complex (BCKD) is an inner-mitochondrial enzyme complex involved in the breakdown of the branched-chain amino acids isoleucine, leucine, and valine.
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DBT Kit ELISA (Dihydrolipoamide Branched Chain Transacylase E2) Kit ELISA
DBT Kit ELISA (Dihydrolipoamide Branched Chain Transacylase E2) Kit ELISA
DBT Kit ELISA (Dihydrolipoamide Branched Chain Transacylase E2) Kit ELISA
DBT Kit ELISA (Dihydrolipoamide Branched Chain Transacylase E2) Kit ELISA
DBT Kit ELISA (Dihydrolipoamide Branched Chain Transacylase E2) Kit ELISA
DBT Kit ELISA (Dihydrolipoamide Branched Chain Transacylase E2) Kit ELISA
DBT profil antigène
Profil protéine
The branched-chain alpha-keto acid dehydrogenase complex (BCKD) is an inner-mitochondrial enzyme complex involved in the breakdown of the branched-chain amino acids isoleucine, leucine, and valine. The BCKD complex is thought to be composed of a core of 24 transacylase (E2) subunits, and associated decarboxylase (E1), dehydrogenase (E3), and regulatory subunits. This gene encodes the transacylase (E2) subunit. Mutations in this gene result in maple syrup urine disease, type 2. Alternatively spliced transcript variants have been described, but their biological validity has not been determined.
Gene names and symbols associated with DBT
- dihydrolipoamide branched chain transacylase E2 (DBT) anticorps
- dihydrolipoamide branched chain transacylase E2 (dbt) anticorps
- dihydrolipoamide branched chain transacylase E2 (CpipJ_CPIJ006326) anticorps
- dihydrolipoamide branched chain transacylase E2 (BDBG_05874) anticorps
- dihydrolipoamide branched chain transacylase E2 (NAEGRDRAFT_78509) anticorps
- dihydrolipoamide branched chain transacylase E2 (VDBG_04820) anticorps
- hypothetical protein (PGTG_17722) anticorps
- dihydrolipoamide branched chain transacylase E2 (Dbt) anticorps
- dihydrolipoamide branched chain transacylase E2 L homeolog (dbt.L) anticorps
- BCATE2 anticorps
- BCKAD-E2 anticorps
- BCKADE2 anticorps
- D3Wsu60e anticorps
- E2 anticorps
- E2b anticorps
- im:7147214 anticorps
- zgc:103768 anticorps
Protein level used designations for DBT
lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial , dihydrolipoamide branched chain transacylase E2 , BCKAD E2 subunit , E2 component of branched chain alpha-keto acid dehydrogenase complex , branched chain acyltransferase, E2 component , branched-chain alpha-keto acid dehydrogenase complex component E2 , dihydrolipoamide acetyltransferase component of branched-chain alpha-keto acid dehydrogenase complex , dihydrolipoyl transacylase , dihydrolipoyllysine-residue (2-methylpropanoyl)transferase , lipoamide acyltransferase component of mitochondrial branched-chain alpha-keto acid dehydrogenase complex , mitochondrial branched chain alpha-keto acid dehydrogenase transacylase subunit (E2b) , BCKAD E2 , BCKAD-E2 , BCKADE2 , branched-chain alpha-ketoacid dehydrogenase, E2 subunit , part of the BCKAD complex , que , mitochondrial branched-chain alpha-keto acid dihydrolipoyl acyltransferase , component of branched chain keto acid dehydrogenase complex
GENE ID | SPECIES |
---|---|
457056 | Pan troglodytes |
100174565 | Pongo abelii |
549717 | Xenopus (Silurana) tropicalis |
711547 | Macaca mulatta |
100050317 | Equus caballus |
100156530 | Sus scrofa |
100346987 | Oryctolagus cuniculus |
6038202 | Culex quinquefasciatus |
8503735 | Ajellomyces dermatitidis SLH14081 |
8862102 | Naegleria gruberi strain NEG-M |
9530433 | Verticillium alfalfae VaMs.102 |
10529473 | Puccinia graminis f. sp. tritici CRL 75-36-700-3 |
1629 | Homo sapiens |
13171 | Mus musculus |
29611 | Rattus norvegicus |
541388 | Danio rerio |
447616 | Xenopus laevis |
395374 | Gallus gallus |
479929 | Canis lupus familiaris |
280759 | Bos taurus |
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