anti-Ethylmalonic Encephalopathy 1 (ETHE1) Anticorps

ETHE1 encodes a sulfur dioxygenase that localizes within the mitochondrial matrix. De plus, nous expédions ETHE1 Protéines (10) et ETHE1 Kits (4) et beaucoup plus de produits pour cette protéine.

afficher tous les anticorps Gène GeneID UniProt
ETHE1 292710  
ETHE1 23474 O95571
ETHE1 66071 Q9DCM0
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Top anti-ETHE1 Anticorps sur anticorps-enligne.fr

Showing 10 out of 64 products:

Catalogue No. Reactivité Hôte Conjugué Application Images Quantité Fournisseur Livraison Prix Détails
Boeuf (Vache) Lapin Inconjugué WB <b>WB Suggested Anti-ETHE1 Antibody Titration: </b>0.2-1 ug/ml<br><b>ELISA Titer: </b>1:62500<br><b>Positive Control: </b>COLO205 cell lysate WB Suggested Anti-ETHE1 <br /> Antibody Titration: 0.2-1 µg/mL ELISA Titer: 1:.2500 <br /> Positive Control: COLO205 cell lysate <br /> ETHE1 is supported by BioGPS gene expression data to be expressed in COLO205 100 μL Connectez-vous pour afficher 2 to 3 Days
$289.00
Détails
Humain Lapin Inconjugué EIA, WB 0.4 mL Connectez-vous pour afficher 6 to 8 Days
$390.50
Détails
Humain Lapin Inconjugué EIA, WB 0.4 mL Connectez-vous pour afficher 6 to 8 Days
$390.50
Détails
Humain Lapin Inconjugué IHC (p), WB Western blot analysis of ETHE1 Antibody (C-term) (ABIN390580) in mouse liver tissue lysates (35 µg/lane).ETHE1 (arrow) was detected using the purified polyclonal antibody. (LEFT)Formalin-fixed and paraffin-embedded human hepatocarcinoma reacted with ETHE1 Antibody (C-term), which was peroxidase-conjugated to the secondary antibody, followed by DAB staining. (RIGHT)Flow cytometric analysis of 293 cells using ETHE1 Antibody (C-term)(bottom histogram) compared to a negative control cell (top histogram). FITC-conjugated goat-anti-rabbit secondary antibodies were used for the analysis. 400 μL Connectez-vous pour afficher 10 to 11 Days
$324.50
Détails
Humain Lapin Inconjugué FACS, IHC (p), WB Western blot analysis of ETHE1 antibody (Center) (ABIN390581) in mouse kidney tissue lysates (35 µg/lane). ETHE1 (arrow) was detected using the purified polyclonal antibody. Flow cytometric analysis of 293 cells using ETHE1 Antibody (Center)(bottom histogram) compared to a negative control cell (top histogram). FITC-conjugated goat-anti-rabbit secondary antibodies were used for the analysis. 400 μL Connectez-vous pour afficher 10 to 11 Days
$324.50
Détails
Boeuf (Vache) Lapin Inconjugué WB 50 μg Connectez-vous pour afficher 7 to 9 Days
$551.83
Détails
Humain Lapin Inconjugué ICC, IF, IHC, IHC (p), WB Immunohistochemistry-Paraffin: ETHE1 Antibody [NBP2-16385] - Immunohistochemical analysis of paraffin-embedded MCF7 xenograft, using antibody at 1:500 dilution. Western Blot: ETHE1 Antibody [NBP2-16385] - Sample (30 ug of whole cell lysate) A: HCT116 12% SDS PAGE gel, diluted at 1:1000. 0.1 mL Connectez-vous pour afficher 8 to 11 Days
$514.63
Détails
Humain Lapin Inconjugué WB Western blot analysis of extracts of various cells, using ETHE1 antibody. 100 μL Connectez-vous pour afficher 16 Days
$334.02
Détails
Humain Lapin Inconjugué ICC, IF, IHC, IHC (p), WB Immunocytochemistry/Immunofluorescence: ETHE1 Antibody [NBP2-16384] - A431 cells were fixed in 2% paraformaldehyde/culture medium at 37C for 30 min. Green: ETHE1 protein stained by ETHE1 antibody diluted at 1:500. Blue: Hoechst 33342 staining. Western Blot: ETHE1 Antibody [NBP2-16384] - Sample (30 ug of whole cell lysate) A: HepG2 12% SDS PAGE gel, diluted at 1:5000. 0.1 mL Connectez-vous pour afficher 8 to 11 Days
$514.63
Détails
Humain Lapin Alexa Fluor 350 IF (p)   100 μL Connectez-vous pour afficher 14 to 21 Days
$405.90
Détails

ETHE1 Anticorps par réactivité, application, clonalité et conjugué

Attributs Application Hôte Clonalité Conjugué
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Plus d’anticorps contre ETHE1 partenaires d’interaction

Human Ethylmalonic Encephalopathy 1 (ETHE1) interaction partners

  1. observations indicate the severe impact of ETHE1 deficiency on cellular physiology and redox state

  2. ETHE1 is a major enzyme regulating endogenous glutathione persulfide /GS-(S)n-H and that its activity is controlled by polysulfidation of the Cys247 residue.

  3. ETHE1 R163W/R163Q mutations are associated with Ethylmalonic encephalopathy.

  4. Case Report: metabolic disturbances in 15-month-old male presenting with typical ethylmalonic encephalopathy associated with a homozygous ETHE1 mutation.

  5. T152I mutation of ETHE1 results in a 3-fold lower activity.

  6. role of the ETHE1 gene product in mitochondrial homeostasis and energy metabolism

  7. Mutations of ETHE1 were detected in all the typical ethylmalonic encephalopathy patients analysed, but no ETHE1 mutations were identified in patients presenting with early onset progressive encephalopathy with ethylmalonic aciduria.

  8. structural comparison of human ETHE1 and At1g53580 from Arabidopsis thaliana

  9. 14 patients with EE were investigated for mutations in the ETHE1 gene. Of the 14 patients, 5 were found to carry novel mutations.

  10. ETHE1 is a mitochondrial sulfur dioxygenase involved in catabolism of sulfide (Montrer SQRDL Anticorps) that accumulates to toxic levels in ethylmalonic encephalopathy.

Mouse (Murine) Ethylmalonic Encephalopathy 1 (ETHE1) interaction partners

  1. Ethe1 deficiency disrupts post translational amino acid modification and mitochondrial metabolic systems.

ETHE1 profil antigène

Profil protéine

This gene encodes a sulfur dioxygenase that localizes within the mitochondrial matrix. The enzyme functions in sulfide catabolism. Mutations in this gene result in ethylmalonic encephalopathy.

Gene names and symbols associated with ETHE1

  • ETHE1, persulfide dioxygenase (Ethe1) anticorps
  • ethylmalonic encephalopathy 1 (ethe1) anticorps
  • ETHE1, persulfide dioxygenase (ETHE1) anticorps
  • ethylmalonic encephalopathy 1 (Ethe1) anticorps
  • 0610025L15Rik anticorps
  • Hsco anticorps
  • YF13H12 anticorps
  • zgc:85680 anticorps

Protein level used designations for ETHE1

protein ETHE1, mitochondrial , ethylmalonic encephalopathy 1 , ethylmalonic encephalopathy protein 1 , hepatoma subtracted clone one protein , persulfide dioxygenase ETHE1, mitochondrial , sulfur dioxygenase ETHE1 , ethylmalonic encephalopathy protein 1 homolog

GENE ID SPECIES
292710 Rattus norvegicus
405865 Danio rerio
426450 Gallus gallus
456093 Pan troglodytes
23474 Homo sapiens
66071 Mus musculus
509150 Bos taurus
612416 Canis lupus familiaris
Fournisseurs de qualité sélectionnés pour anti-ETHE1 (ETHE1) Anticorps
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