anti-LMBR1 Domain Containing 1 (LMBRD1) Anticorps

LMBRD1 encodes a lysosomal membrane protein that may be involved in the transport and metabolism of cobalamin. De plus, nous expédions LMBR1 Domain Containing 1 Protéines (4) et LMBR1 Domain Containing 1 Kits (1) et beaucoup plus de produits pour cette protéine.

afficher tous les anticorps Gène GeneID UniProt
LMBRD1 55788 Q9NUN5
LMBRD1 68421 Q8K0B2
LMBRD1 246046 Q6AZ61
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Top anti-LMBR1 Domain Containing 1 Anticorps sur anticorps-enligne.fr

Showing 10 out of 18 products:

Catalogue No. Reactivité Hôte Conjugué Application Images Quantité Fournisseur Livraison Prix Détails
Humain Lapin Inconjugué EIA, WB   0.1 mg Connectez-vous pour afficher 12 to 15 Days
$469.32
Détails
Humain Lapin Inconjugué IHC (p), ELISA, WB Human Breast: Formalin-Fixed, Paraffin-Embedded (FFPE) Human Colon, Myenteric Plexus: Formalin-Fixed, Paraffin-Embedded (FFPE) 50 μg Connectez-vous pour afficher 7 to 9 Days
$484.00
Détails
Humain Lapin Inconjugué EIA, IHC (p), WB Human Breast: Formalin-Fixed, Paraffin-Embedded (FFPE) Human Colon, Myenteric Plexus: Formalin-Fixed, Paraffin-Embedded (FFPE) 50 μg Connectez-vous pour afficher 6 to 8 Days
$390.50
Détails
Humain Lapin Inconjugué IF, IHC, ELISA, WB   100 μg Connectez-vous pour afficher 15 to 19 Days
$511.06
Détails
Humain Lapin Inconjugué IHC, ELISA, WB 0.1 mg Connectez-vous pour afficher 2 to 3 Days
$350.00
Détails
Humain Lapin Inconjugué ELISA, ICC, IF, IHC, WB Western Blot: LMBRD1 Antibody [NBP1-76494] - Human brain tissue lysate with LMBRD1 antibody at 1 ug/mL. Immunocytochemistry/Immunofluorescence: LMBRD1 Antibody [NBP1-76494] - Immunofluorescence of LMBRD1 in human brain tissue with LMBRD1 antibody at 20 ug/mL. 0.1 mg Connectez-vous pour afficher 8 to 11 Days
$485.88
Détails
Humain Lapin Inconjugué WB   100 μL Connectez-vous pour afficher 2 to 3 Days
$376.44
Détails
Humain Lapin Inconjugué IHC, IHC (p), WB Western Blot: LMBRD1 Antibody [NBP1-88729] - Lane 1: Marker [kDa] 250, 130, 95, 72, 55, 36, 28, 17, 10.Lane 2: Negative control (vector only transfected HEK293T lysate).Lane 3: Over-expression lysate (Co-expressed with a C-terminal myc-DDK tag (~3.1 kDa) in mammalian HEK293T cells, LY413120) Immunohistochemistry-Paraffin: LMBRD1 Antibody [NBP1-88729] - Staining of human hippocampus shows strong cytoplasmic positivity in neuronal cells. 0.1 mL Connectez-vous pour afficher 10 to 13 Days
$491.63
Détails
Humain Lapin Inconjugué IF, IHC, ELISA, WB   100 μg Connectez-vous pour afficher 11 to 16 Days
$578.29
Détails
Humain Lapin Inconjugué IHC, ELISA, WB   50 μg Connectez-vous pour afficher 11 to 16 Days
$762.14
Détails

LMBRD1 Anticorps par réactivité, application, clonalité et conjugué

Attributs Application Hôte Clonalité
Human


Mouse (Murine)


Rat (Rattus)


Plus d’anticorps contre LMBR1 Domain Containing 1 partenaires d’interaction

Human LMBR1 Domain Containing 1 (LMBRD1) interaction partners

  1. endogenous ABCD4 (Montrer ABCD4 Anticorps) was localized to both lysosomes and the ER, and its lysosomal localization was disturbed by knockout of LMBRD1

  2. Data suggest that ABCD4 lysosomal targeting depends on co-expression of and interaction with LMBRD1; mutations in LMBRD1 and ABCD4 that result in cobalamin metabolism disorders cblF and cblJ (or mutations in ATPase domain) disrupt interactions between LMBRD1 and ABCD4. (LMBRD1 = nuclear export signal-interacting protein; ABCD4 = ATP-binding cassette, sub-family D (ALD), member 4)

  3. Results propose a model whereby membrane-bound LMBD1 and ABCD4 (Montrer ABCD4 Anticorps) facilitate the vectorial delivery of lysosomal vitamin B12 (Montrer NDUFB3 Anticorps) to cytoplasmic MMACHC (Montrer MMACHC Anticorps).

  4. LMBD1 plays an imperative role in mediating and regulating the endocytosis of the IR.

  5. These data indicate that by forming complexes with lamin A/C (Montrer LMNA Anticorps) and nucleoporins, NESI facilitates the CRM1 (Montrer XPO1 Anticorps)-independent nuclear export of large hepatitis delta antigen.

  6. novel mutations in LMBRD1 in three patients

  7. LMBRD1: the gene for the cblF defect of vitamin B metabolism.

  8. a LMBRD1 mutation causes the cblF defect of vitamin B(12) metabolism in a Turkish patient [case report]

  9. LMBRD1 is the gene underlying the cblF defect of cobalamin metabolism and suggests that LMBD1 is a lysosomal membrane exporter for cobalamin.

Mouse (Murine) LMBR1 Domain Containing 1 (LMBRD1) interaction partners

  1. the physiological function of LMBRD1 during embryogenesis, is reported.

  2. LMBD1 plays an imperative role in mediating and regulating the endocytosis of the IR.

LMBR1 Domain Containing 1 (LMBRD1) profil antigène

Profil protéine

This gene encodes a lysosomal membrane protein that may be involved in the transport and metabolism of cobalamin. This protein also interacts with the large form of the hepatitis delta antigen and may be required for the nucleocytoplasmic shuttling of the hepatitis delta virus. Mutations in this gene are associated with the vitamin B12 metabolism disorder termed, homocystinuria-megaloblastic anemia complementation type F.

Gene names and symbols associated with LMBRD1

  • LMBR1 domain containing 1 (lmbrd1) anticorps
  • LMBR1 domain containing 1 (LMBRD1) anticorps
  • LMBR1 domain containing 1 (MCYG_07794) anticorps
  • LMBR1 domain containing 1 (Lmbrd1) anticorps
  • LMBR1 domain containing 1 L homeolog (lmbrd1.L) anticorps
  • 0910001K20Rik anticorps
  • AV347960 anticorps
  • C6orf209 anticorps
  • fc08a03 anticorps
  • LMBD1 anticorps
  • MAHCF anticorps
  • MGC89794 anticorps
  • NESI anticorps
  • wu:fc08a03 anticorps
  • zgc:103471 anticorps

Protein level used designations for LMBRD1

LMBR1 domain-containing protein 1 , probable lysosomal cobalamin transporter , LMBR1 domain containing 1 , HDAg-L-interacting protein NESI , hepatitis delta antigen-L interacting protein , liver regeneration p-53 related protein , nuclear export signal-interacting protein , protein N90b

GENE ID SPECIES
323720 Danio rerio
474955 Canis lupus familiaris
714710 Macaca mulatta
736319 Pan troglodytes
779630 Xenopus (Silurana) tropicalis
9226393 Arthroderma otae CBS 113480
100057167 Equus caballus
100153685 Sus scrofa
55788 Homo sapiens
68421 Mus musculus
246046 Rattus norvegicus
510495 Bos taurus
421874 Gallus gallus
398468 Xenopus laevis
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