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GAA anticorps (AA 350-450)

GAA Reactivité: Humain WB, IP, IF Hôte: Lapin Polyclonal unconjugated
N° du produit ABIN6140865
  • Antigène Voir toutes GAA Anticorps
    GAA (Glucosidase, Alpha, Acid (GAA))
    Épitope
    • 15
    • 9
    • 6
    • 6
    • 4
    • 3
    • 3
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    AA 350-450
    Reactivité
    • 47
    • 22
    • 21
    • 2
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    Humain
    Hôte
    • 47
    • 4
    Lapin
    Clonalité
    • 47
    • 4
    Polyclonal
    Conjugué
    • 26
    • 5
    • 4
    • 3
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    Cet anticorp GAA est non-conjugé
    Application
    • 47
    • 19
    • 15
    • 13
    • 13
    • 8
    • 7
    • 4
    • 3
    • 2
    • 1
    • 1
    Western Blotting (WB), Immunoprecipitation (IP), Immunofluorescence (IF)
    Séquence
    VVQQYLDVVG YPFMPPYWGL GFHLCRWGYS STAITRQVVE NMTRAHFPLD VQWNDLDYMD SRRDFTFNKD GFRDFPAMVQ ELHQGGRRYM MIVDPAISSS G
     Réactivité croisée
    Humain, Souris, Rat
    Attributs du produit
    Polyclonal Antibodies
    Purification
    Affinity purification
    Immunogène
    A synthetic peptide corresponding to a sequence within amino acids 350-450 of human GAA (NP_000143.2).
    Isotype
    IgG
    Top Product
    Discover our top product GAA Anticorps primaire
  • Indications d'application
    WB,1:500 - 1:2000,IF,1:50 - 1:200,IP,1:50 - 1:200
    Commentaires

    HIGH QUALITY

    Restrictions
    For Research Use only
  • Format
    Liquid
    Buffer
    PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
    Agent conservateur
    Sodium azide
    Précaution d'utilisation
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    Stock
    -20 °C
    Stockage commentaire
    Store at -20°C. Avoid freeze / thaw cycles.
  • Antigène
    GAA (Glucosidase, Alpha, Acid (GAA))
    Autre désignation
    GAA (GAA Produits)
    Synonymes
    anticorps LYAG, anticorps E430018M07Rik, anticorps glucosidase alpha, acid, anticorps glucosidase, alpha, acid, anticorps transmembrane and coiled-coil domain family 1, anticorps glucosidase, alpha; acid (Pompe disease, glycogen storage disease type II), anticorps GAA, anticorps Gaa, anticorps TMCC1, anticorps gaa
    Sujet
    This gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants.,GAA,LYAG,Cancer,Signal Transduction,Endocrine & Metabolism,GAA
    Poids moléculaire
    105 kDa
    ID gène
    2548
    UniProt
    P10253
    Pathways
    Cellular Glucan Metabolic Process
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