HMGCL anticorps (3-Hydroxymethyl-3-Methylglutaryl-CoA Lyase) (Biotin)

Details for Product anti-HMGCL Antibody No. ABIN709183
Antigène
  • Afu7g01720
  • AO090038000541
  • AW476067
  • HL
  • zgc:56248
  • 3-hydroxymethyl-3-methylglutaryl-CoA lyase S homeolog
  • 3-hydroxymethyl-3-methylglutaryl-CoA lyase
  • 3-hydroxymethyl-3-methylglutaryl-Coenzyme A lyase
  • 3-hydroxy-3-methylglutaryl-Coenzyme A lyase
  • hmgcl.S
  • HMGCL
  • AFUA_7G01720
  • NFIA_114450
  • ACLA_065820
  • AOR_1_910074
  • PMAA_004600
  • TSTA_103060
  • ARB_04874
  • TRV_06573
  • Hmgcl
  • hmgcl
Reactivité
Humain, Souris, Rat (Rattus)
106
42
38
9
4
3
3
3
2
2
1
1
1
Hôte
Lapin
102
5
Clonalité
Polyclonal
Conjugué
Cet anticorp HMGCL est conjugé à/à la Biotin
5
5
5
4
4
4
2
2
2
2
2
2
1
1
1
1
1
Application
Immunohistochemistry (Paraffin-embedded Sections) (IHC (p)), Western Blotting (WB)
85
48
25
13
6
6
4
2
1
1
1
1
Options
Immunogène KLH conjugated synthetic peptide derived from human HMGCL
Isotype IgG
Purification Purified by Protein A.
Plasmids, Primers & others Plasmids, Primers & others HMGCL products on genomics-online (e.g. as negative or positive controls)
Antigène
Autre désignation Hmgcl (HMGCL Antibody Extrait)
Sujet

Hydroxymethylglutaryl-CoA lyase (HMGCL) is found in fibroblasts, liver and lymphoblasts. It has a role in ketogenesis and leucine catabolism. Defects in HMGCL are the cause of 3-hydroxy-3-methylglutaryl-CoA lyase deficiency (hydroxymethylglutaricaciduria), an autosomal recessive disease which can lead to hypoglycemia and coma.

Synonyms: 3 hydroxy 3 methylglutaryl CoA lyase, 3 hydroxy 3 methylglutaryl Coenzyme A lyase, 3 hydroxymethyl 3 methylglutaryl Coenzyme A lyase hydroxymethylglutaricaciduria, 3 hydroxymethyl 3 methylglutaryl Coenzyme A lyase, 3-hydroxy-3-methylglutarate-CoA lyase, HL, HMG CoA lyase, HMG CoA Lyase Deficiency, HMG-CoA lyase, HMGCL, HMGCL_HUMAN, Hydroxymethylglutaricaciduria, Hydroxymethylglutaryl CoA lyase, Hydroxymethylglutaryl CoA lyase mitochondrial, Hydroxymethylglutaryl-CoA lyase, mitochondrial, MS725, OTTHUMP00000044830.

ID gène 2835
Indications d'application WB 1:100-1000
IHC-P 1:100-500
Restrictions For Research Use only
Format Liquid
Concentration 1 μg/μL
Buffer Aqueous buffered solution containing 1 % BSA, 50 % glycerol and 0.09 % sodium azide.
Agent conservateur Sodium azide
Précaution d'utilisation This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
Stock 4 °C
Stockage commentaire Store at 4°C
Date de péremption 12 months
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