ALDOA Protein (AA 2-364, full length) (GST tag)
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- Antigène Voir toutes ALDOA Protéines
- ALDOA (Aldolase A, Fructose-Bisphosphate (ALDOA))
- Type de proteíne
- Recombinant
- Attributs du protein
- AA 2-364, full length
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Origine
- Humain
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Source
- Escherichia coli (E. coli)
- Purification/Conjugué
- Cette ALDOA protéine est marqué à la GST tag.
- Application
- SDS-PAGE (SDS), Western Blotting (WB), ELISA
- Séquence
- PYQYPALTPE QKKELSDIAH RIVAPGKGIL AADESTGSIA KRLQSIGTEN TEENRRFYRQ LLLTADDRVN PCIGGVILFH ETLYQKADDG RPFPQVIKSK GGVVGIKVDK GVVPLAGTNG ETTTQGLDGL SERCAQYKKD GADFAKWRCV LKIGEHTPSA LAIMENANVL ARYASICQQN GIVPIVEPEI LPDGDHDLKR CQYVTEKVLA AVYKALSDHH IYLEGTLLKP NMVTPGHACT QKFSHEEIAM ATVTALRRTV PPAVTGITFL SGGQSEEEAS INLNAINKCP LLKPWALTFS YGRALQASAL KAWGGKKENL KAAQEEYVKR ALANSLACQG KYTPSGQAGA AASESLFVSN HAY
- Pureté
- 95 %
- Top Product
- Discover our top product ALDOA Protéine
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- Restrictions
- For Research Use only
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- Format
- Lyophilized
- Buffer
- 6M guanidine hydrochloride, 20mM Tris
- Stock
- 4 °C
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- Antigène
- ALDOA (Aldolase A, Fructose-Bisphosphate (ALDOA))
- Autre désignation
- Fructose-Bisphosphate Aldolase A Protein (ALDOA Produits)
- Synonymes
- ALDA Protein, GSD12 Protein, aldoa Protein, cb79 Protein, sb:cb79 Protein, wu:fa28b10 Protein, wu:fb10b11 Protein, ALDOA Protein, Aldo-1 Protein, Aldo1 Protein, RNALDOG5 Protein, hm:zeh0036 Protein, zgc:77696 Protein, aldolase, fructose-bisphosphate A Protein, aldolase a, fructose-bisphosphate, a Protein, aldolase, fructose-bisphosphate A S homeolog Protein, aldolase A, fructose-bisphosphate Protein, aldolase a, fructose-bisphosphate, b Protein, ALDOA Protein, aldoaa Protein, aldoa Protein, aldoa.S Protein, Aldoa Protein, aldoab Protein
- Sujet
- Background: Defects in ALDOA are the cause of glycogen storage disease type 12 (GSD12) [MIM:611881], also known as red cell aldolase deficiency. A metabolic disorder associated with increased hepatic glycogen and hemolytic anemia. It may lead to myopathy with exercise intolerance and rhabdomyolysis. Synonyms: Lung cancer antigen NY-LU-1 Muscle-type aldolase.
- Poids moléculaire
- 66.7 kD
- NCBI Accession
- NM_000034
- UniProt
- P04075
- Pathways
- Ribonucleoside Biosynthetic Process
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