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Adenylosuccinate Lyase Produits

(Adenylosuccinate Lyase (ADSL))

Catégories

Adenylsuccinate lyase is involved in both de novo synthesis of purines and formation of adenosine monophosphate from inosine monophosphate. It catalyzes two reactions in AMP biosynthesis: the removal of a fumarate from succinylaminoimidazole carboxamide (SAICA) ribotide to give aminoimidazole carboxamide ribotide (AICA) and removal of fumarate from adenylosuccinate to give AMP. Adenylosuccinase deficiency results in succinylpurinemic autism, psychomotor retardation, and , in some cases, growth retardation associated with muscle wasting and epilepsy. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jul 2008].

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Catégories Adenylosuccinate Lyase en vedette

Adenylosuccinate Lyase Anticorps

High quality antibodies with extensive validation data.

Adenylosuccinate Lyase Kits ELISA

Reliable ELISA kits for a wide range of species.

Adenylosuccinate Lyase Protéines

Proteins for various applications incl. WB, ELISA, IF etc.

Adenylosuccinate Lyase recommandé Anticorps

Produit
Reactivity
Application
Validations
N° du produit
Quantité
Fiche technique
Reactivity Human
Application WB, IHC, ELISA
Validations
  • (2)
N° du produit ABIN7143352
Quantité 100 μL
Fiche technique Fiche technique
Reactivity Human, Mouse, Rat
Application WB, IF
Validations
  • (2)
N° du produit ABIN7262084
Quantité 200 μL
Fiche technique Fiche technique
Reactivity Human
Application WB
Validations
  • (2)
N° du produit ABIN947541
Quantité 100 μg
Fiche technique Fiche technique

Adenylosuccinate Lyase recommandé Kits ELISA

Produit
Reactivity
Analytical Method
Validations
N° du produit
Quantité
Fiche technique
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
N° du produit ABIN6964640
Quantité 96 tests
Fiche technique Fiche technique
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
N° du produit ABIN6730398
Quantité 96 tests
Fiche technique Fiche technique
Reactivity Mouse
Analytical Method
Validations
N° du produit ABIN1120655
Quantité 96 tests
Fiche technique Fiche technique

Adenylosuccinate Lyase recommandé Protéines

Produit
Reactivity
Source
Validations
N° du produit
Quantité
Fiche technique
Reactivity Human
Source Wheat germ
Validations
  • (1)
N° du produit ABIN1344500
Quantité 10 μg
Fiche technique Fiche technique
Reactivity Human
Source Escherichia coli (E. coli)
Validations
  • (1)
N° du produit ABIN7121722
Quantité 50 μg
Fiche technique Fiche technique
Reactivity Human
Source Insect Cells
Validations
  • (1)
N° du produit ABIN3086712
Quantité 1 mg
Fiche technique Fiche technique

Dernières publications sur nos produits Adenylosuccinate Lyase

van Straten, van Steenbeek, Grinwis, Favier, Kummeling, van Gils, Fieten, Groot Koerkamp, Holstege, Rothuizen, Spee: "Aberrant expression and distribution of enzymes of the urea cycle and other ammonia metabolizing pathways in dogs with congenital portosystemic shunts." dans: PLoS ONE, Vol. 9, Issue 6, pp. e100077, (2014) (PubMed).

Sadasivan, Vasamsetti, Singh, Siddaraju, Khan, Oommen, Jagannath, Rao: "Modulation of de novo purine biosynthesis leads to activation of AMPK and results in improved glucose handling and insulin sensitivity." dans: Journal of diabetes and metabolic disorders, Vol. 13, pp. 51, (2014) (PubMed).

Baresova, Skopova, Sikora, Patterson, Sovova, Zikanova, Kmoch: "Mutations of ATIC and ADSL affect purinosome assembly in cultured skin fibroblasts from patients with AICA-ribosiduria and ADSL deficiency." dans: Human molecular genetics, Vol. 21, Issue 7, pp. 1534-43, (2012) (PubMed).

Stadler, Hjelmare, Neumann, Jonasson, Pepperkok, Uhlén, Lundberg: "Systematic validation of antibody binding and protein subcellular localization using siRNA and confocal microscopy." dans: Journal of proteomics, Vol. 75, Issue 7, pp. 2236-51, (2012) (PubMed).

Blumstein, Faundez, Nakatsu, Saito, Ohno, Kelly: "The neuronal form of adaptor protein-3 is required for synaptic vesicle formation from endosomes." dans: The Journal of neuroscience : the official journal of the Society for Neuroscience, Vol. 21, Issue 20, pp. 8034-42, (2001) (PubMed).

Zhen, Jiang, Feng, Bright, Peden, Seymour, Novak, Elliott, Gorin, Robinson, Swank: "Abnormal expression and subcellular distribution of subunit proteins of the AP-3 adaptor complex lead to platelet storage pool deficiency in the pearl mouse." dans: Blood, Vol. 94, Issue 1, pp. 146-55, (1999) (PubMed).

Ooi, Moreira, DellAngelica, Poy, Wassarman, Bonifacino: "Altered expression of a novel adaptin leads to defective pigment granule biogenesis in the Drosophila eye color mutant garnet." dans: The EMBO journal, Vol. 16, Issue 15, pp. 4508-18, (1997) (PubMed).

Synonymes et noms alternatifs relatifs à Adenylosuccinate Lyase

adenylosuccinate lyase (ADSL), adenylosuccinate lyase (adsl), adenylosuccinate lyase L homeolog (adsl.L), adenylosuccinate lyase (ASL), adenylosuccinate lyase (purB), adenylosuccinase; ASL (purB), adenylosuccinate lyase (purB,adsL), adenylosuccinate lyase (Mrub_2293), adenylosuccinate lyase (MMAH_RS02975), adenylosuccinate lyase (Arnit_0089), adenylosuccinate lyase (Mesil_1058), adenylosuccinate lyase (Slip_0597), adenylosuccinate lyase (Trad_2452), adenylosuccinate lyase (Deba_0652), adenylosuccinate lyase (Toce_1174), Adenylosuccinate lyase (Acear_2324), Adenylosuccinate lyase (Igag_0272), adenylosuccinate lyase (Saut_2156), Adenylosuccinate lyase (Fbal_1996), adenylosuccinate lyase (Ndas_2434), adenylosuccinate lyase (Ilyop_0196), adenylosuccinate lyase (Lbys_2961), adenylosuccinate lyase (MFER_RS02920), adenylosuccinate lyase (Palpr_2192), adenylosuccinate lyase (Calni_0061), adenylosuccinate lyase (Ftrac_3746), L-Aspartase-like family protein (AT1G36280), Adenylosuccinate lyase (Olsu_1764), adenylosuccinate lyase (Adsl), Adl, adsL, AMPS, ASASE, ASL, Asl, F15C21.8, F15C21_8, fi60b04, MGC53383, MGC69239, purB, wu:fi60b04, zgc:56061

Protein level used designations for Adenylosuccinate Lyase

  • adenylosuccinate lyase
  • Adenylosuccinate lyase
  • adenylosuccinate lyase-like
  • adenylosuccinase
  • ASase
  • adenylosuccinate lyase 1
  • test
  • ASL
  • adenysuccinate lyase
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