HADH anticorps (AA 57-314)

N° du produit ABIN2468091

Cet anticorps anti-HADH est un anticorps Poulet Polyclonal détectant HADH dans WB. Adapté pour Humain, Souris et Rat.

Aperçu rapide pour HADH anticorps (AA 57-314) (ABIN2468091)

Antigène: HADH (Hydroxyacyl-CoA Dehydrogenase (HADH))

Reactivité: Humain, Souris, Rat

Hôte: Poulet

Clonalité: Polyclonal

Conjugué: Cet anticorp HADH est non-conjugé

Application: Western Blotting (WB)

Détail du produit anti-HADH anticorps

Épitope: AA 57-314

Purification: Immunoaffinity Purified

Information d'application

Indications d'application: Short chain 3-hydroxyacyl-CoA dehydrogenase, mitochondrial antibody can be used for the detection of Short chain 3-hydroxyacyl-CoA dehydrogenase, mitochondrial by Western Blot.

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1 mg/mL

Buffer: Phosphate-Buffered Saline. No preservatives added.

Agent conservateur: Without preservative

Conseil sur la manipulation: As with all antibodies care should be taken to avoid repeated freeze thaw cycles. Antibodies should not be exposed to prolonged high temperatures.

Stock: 4 °C/-20 °C

Stockage commentaire: HADHSC antibody can be stored at 4 °C for short term (weeks). Long term storage should be at -20 °C.

Détails sur HADH

Antigène: HADH (Hydroxyacyl-CoA Dehydrogenase (HADH))

Autre désignation: HADHSC

Sujet: FUNCTION: Plays an essential role in the mitochondrial beta-oxidation of short chain fatty acids. Exerts it highest activity toward 3-hydroxybutyryl-CoA.

DISEASE: Defects in HADHSC are the cause of 3-alpha-hydroxyacyl-CoA dehydrogenase deficiency (HAD deficiency) [MIM:609609]. HAD deficiency is a metabolic disorder with various clinical presentations including hypoglycemia, hepatoencephalopathy, myopathy or cardiomyopathy, and in some cases sudden death.

Poids moléculaire: 34.3 kDa (calculated)

ID gène: 3033

NCBI Accession: NP_005318

UniProt: Q16836

Pathways: Negative Regulation of Hormone Secretion, Monocarboxylic Acid Catabolic Process