SGSH anticorps (C-Term)

N° du produit ABIN2783228

Détail du produit anti-SGSH anticorps

Antigène: SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))

Épitope: C-Term

Reactivité: Humain, Rat, Souris, Boeuf (Vache), Cheval, Chien

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp SGSH est non-conjugé

Application: Western Blotting (WB)

Séquence: ARWELYDRSR DPHETQNLAT DPRFAQLLEM LRDQLAKWQW ETHDPWVCAP

Homologie: Cow: 79%, Dog: 86%, Horse: 93%, Human: 100%, Mouse: 79%, Rat: 79%

Attributs du produit: This is a rabbit polyclonal antibody against SGSH. It was validated on Western Blot.

Purification: Affinity Purified

Immunogène: The immunogen is a synthetic peptide directed towards the C-terminal region of human SGSH

Information d'application

Indications d'application: Optimal working dilution should be determined by the investigator.

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1 mg/mL

Buffer: Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Conseil sur la manipulation: Avoid repeat freeze-thaw cycles.

Stock: -20 °C

Stockage commentaire: For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.

Détails sur SGSH

Antigène: SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))

Autre désignation: SGSH (SGSH Produits)

Synonymes: anticorps HSS, anticorps MPS3A, anticorps SFMD, anticorps 4632406A19Rik, anticorps N-sulfoglucosamine sulfohydrolase, anticorps N-sulfoglucosamine sulfohydrolase (sulfamidase), anticorps SGSH, anticorps Sgsh

Sujet: This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.
Alias Symbols: HSS, SFMD, MPS3A
Protein Size: 299

Poids moléculaire: 32 kDa

ID gène: 6448

NCBI Accession: NM_000199, NP_000190

UniProt: P51688

Pathways: Glycosaminoglycan Metabolic Process