ALG1 anticorps (C-Term)
Aperçu rapide pour ALG1 anticorps (C-Term) (ABIN2783688)
Antigène
Voir toutes ALG1 AnticorpsReactivité
Hôte
Clonalité
Conjugué
Application
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Épitope
- C-Term
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Séquence
- VKHEENGLVF EDSEELAAQL QMLFSNFPDP AGKLNQFRKN LRESQQLRWD
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Homologie
- Cow: 86%, Dog: 93%, Guinea Pig: 92%, Human: 100%, Mouse: 86%, Rabbit: 86%, Rat: 92%
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Attributs du produit
- This is a rabbit polyclonal antibody against ALG1. It was validated on Western Blot.
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Purification
- Affinity Purified
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Immunogène
- The immunogen is a synthetic peptide directed towards the C-terminal region of human ALG1
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Restrictions
- For Research Use only
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Format
- Liquid
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Concentration
- 1 mg/mL
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Buffer
- Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
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Agent conservateur
- Sodium azide
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Précaution d'utilisation
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Conseil sur la manipulation
- Avoid repeat freeze-thaw cycles.
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Stock
- -20 °C
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Stockage commentaire
- For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
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: "A severe human metabolic disease caused by deficiency of the endoplasmatic mannosyltransferase hALG11 leads to congenital disorder of glycosylation-Ip." dans: Human molecular genetics, Vol. 19, Issue 8, pp. 1413-24, (2010) (PubMed).
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- ALG1 (Chitobiosyldiphosphodolichol beta-Mannosyltransferase (ALG1))
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Autre désignation
- ALG1
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Sujet
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The enzyme encoded by this gene catalyzes the first mannosylation step in the biosynthesis of lipid-linked oligosaccharides. This gene is mutated in congenital disorder of glycosylation type Ik.
Alias Symbols: HMT1, MT-1, CDG1K, HMAT1, HMT-1, Mat-1, hMat-1
Protein Size: 353 -
Poids moléculaire
- 38 kDa
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ID gène
- 56052
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NCBI Accession
- NM_019109, NP_061982
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UniProt
- B4DP08
Antigène
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