ALG1 anticorps (C-Term)

N° du produit ABIN2783688

Cet anticorps Lapin Polyclonal détecte spécifiquement ALG1 dans WB. Il présente une réactivité avec des échantillons de Humain, Souris, Rat, Lapin, Boeuf (Vache), Chien et Cobaye.Il a été cité dans 1 publication.

Aperçu rapide pour ALG1 anticorps (C-Term) (ABIN2783688)

Antigène: ALG1 (Chitobiosyldiphosphodolichol beta-Mannosyltransferase (ALG1))

Reactivité: Humain, Souris, Rat, Lapin, Boeuf (Vache), Chien, Cobaye

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp ALG1 est non-conjugé

Application: Western Blotting (WB)

Détail du produit anti-ALG1 anticorps

Épitope: C-Term

Fonction: ALG1 Antibody - C-terminal region

Séquence: VKHEENGLVF EDSEELAAQL QMLFSNFPDP AGKLNQFRKN LRESQQLRWD

Homologie: Cow: 86%, Dog: 93%, Guinea Pig: 92%, Human: 100%, Mouse: 86%, Rabbit: 86%, Rat: 92%

Attributs du produit: This is a rabbit polyclonal antibody against ALG1. It was validated on Western Blot.

Purification: Affinity Purified

Immunogène: The immunogen is a synthetic peptide directed towards the C-terminal region of human ALG1

Information d'application

Indications d'application: Optimal working dilution should be determined by the investigator.

Commentaires:

We also sell a specific blocking peptide that can be used in combination with this antibody. You can find the blocking peptide under AAP49252-100UG

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 0.5 mg/mL

Buffer: Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Conseil sur la manipulation: prevent freeze-thaw cycles

Stock: 4 °C,-20 °C

Stockage commentaire: For short term use, store at 2-8C up to 1 week. For long term storage, store at -20 °C in small aliquots to prevent freeze-thaw cycles.

Références pour anticorps anti-ALG1 (ABIN2783688)

Rind, Schmeiser, Thiel, Absmanner, Lübbehusen, Hocks, Apeshiotis, Wilichowski, Lehle, Körner: "A severe human metabolic disease caused by deficiency of the endoplasmatic mannosyltransferase hALG11 leads to congenital disorder of glycosylation-Ip." dans: Human molecular genetics, Vol. 19, Issue 8, pp. 1413-24, (2010) (PubMed).

Détails sur ALG1

Antigène: ALG1 (Chitobiosyldiphosphodolichol beta-Mannosyltransferase (ALG1))

Autre désignation: ALG1

Sujet:

Background Information: The enzyme encoded by this gene catalyzes the first mannosylation step in the biosynthesis of lipid-linked oligosaccharides. This gene is mutated in congenital disorder of glycosylation type Ik.

Gene Name: ALG1, chitobiosyldiphosphodolichol beta-mannosyltransferase

Alternative Symbols: HMT1, MT-1, CDG1K, HMAT1, HMT-1, Mat-1, hMat-1

Protein Name: chitobiosyldiphosphodolichol beta-mannosyltransferase

Poids moléculaire: 38kDa

ID gène: 56052

NCBI Accession: NP_061982

UniProt: B4DP08