GBE1 anticorps (N-Term)
Aperçu rapide pour GBE1 anticorps (N-Term) (ABIN2789854)
Antigène
Voir toutes GBE1 AnticorpsReactivité
Hôte
Clonalité
Conjugué
Application
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Épitope
- N-Term
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Fonction
- GBE1 Antibody - N-terminal region
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Séquence
- IHWDPEHSYE FKHSRPKKPR SLRIYESHVG ISSHEGKVAS YKHFTCNVLP
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Homologie
- Cow: 83%, Dog: 83%, Guinea Pig: 85%, Horse: 92%, Human: 100%, Mouse: 92%, Rabbit: 92%, Rat: 92%
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Attributs du produit
- This is a rabbit polyclonal antibody against GBE1. It was validated on Western Blot.
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Purification
- Affinity Purified
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Indications d'application
- Optimal working dilution should be determined by the investigator.
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Commentaires
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We also sell a specific blocking peptide that can be used in combination with this antibody. You can find the blocking peptide under AAP64504-100UG
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Restrictions
- For Research Use only
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Format
- Liquid
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Concentration
- 0.5 mg/mL
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Buffer
- Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
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Agent conservateur
- Sodium azide
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Précaution d'utilisation
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Conseil sur la manipulation
- prevent freeze-thaw cycles
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Stock
- 4 °C,-20 °C
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Stockage commentaire
- For short term use, store at 2-8C up to 1 week. For long term storage, store at -20 °C in small aliquots to prevent freeze-thaw cycles.
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- GBE1 (Glucan (1,4-alpha-), Branching Enzyme 1 (GBE1))
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Autre désignation
- GBE1
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Sujet
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Background Information: The protein encoded by this gene is a glycogen branching enzyme that catalyzes the transfer of alpha-1,4-linked glucosyl units from the outer end of a glycogen chain to an alpha-1,6 position on the same or a neighboring glycogen chain. Branching of the chains is essential to increase the solubility of the glycogen molecule and, consequently, in reducing the osmotic pressure within cells. Highest level of this enzyme are found in liver and muscle. Mutations in this gene are associated with glycogen storage disease IV (also known as Andersen's disease).
Gene Name: Glucan (1,4-alpha-), branching enzyme 1
Alternative Symbols: GBE, APBD, GSD4
Protein Name: 1,4-alpha-glucan-branching enzyme
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Poids moléculaire
- 80kDa
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ID gène
- 2632
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NCBI Accession
- NP_000149
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UniProt
- Q04446
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Pathways
- Cellular Glucan Metabolic Process
Antigène
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