BLOC1S3 anticorps (N-Term)
Aperçu rapide pour BLOC1S3 anticorps (N-Term) (ABIN2790099)
Antigène
Voir toutes BLOC1S3 AnticorpsReactivité
Hôte
Clonalité
Conjugué
Application
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Épitope
- N-Term
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Fonction
- BLOC1S3 Antibody - N-terminal region
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Séquence
- RGRPTGLRVA GEAAETDSEP EPEPEPTAAP RDLPPLVVQR ESAEEAWGTE
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Homologie
- Cow: 93%, Dog: 86%, Goat: 79%, Guinea Pig: 86%, Horse: 79%, Human: 100%, Mouse: 100%, Rat: 100%, Sheep: 79%, Zebrafish: 79%
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Attributs du produit
- This is a rabbit polyclonal antibody against BLOC1S3. It was validated on Western Blot.
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Purification
- Affinity Purified
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Indications d'application
- Optimal working dilution should be determined by the investigator.
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Commentaires
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We also sell a specific blocking peptide that can be used in combination with this antibody. You can find the blocking peptide under AAP65298-100UG
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Restrictions
- For Research Use only
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Format
- Liquid
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Concentration
- 0.5 mg/mL
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Buffer
- Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
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Agent conservateur
- Sodium azide
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Précaution d'utilisation
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Conseil sur la manipulation
- prevent freeze-thaw cycles
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Stock
- 4 °C,-20 °C
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Stockage commentaire
- For short term use, store at 2-8C up to 1 week. For long term storage, store at -20 °C in small aliquots to prevent freeze-thaw cycles.
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- BLOC1S3 (Biogenesis of Lysosomal Organelles Complex-1, Subunit 3 (BLOC1S3))
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Autre désignation
- BLOC1S3
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Sujet
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Targeted Subunit: 3
Background Information: This gene encodes a protein that is a component of the BLOC1 multi-subunit protein complex. This complex is necessary for the biogenesis of specialized organelles of the endosomal-lysosomal system, including platelet dense granules and melanosomes. Mutations in this gene cause Hermansky-Pudlak syndrome 8, a disease characterized by lysosomal storage defects, bleeding due to platelet storage pool deficiency, and oculocutaneous albinism.
Gene Name: Biogenesis of lysosomal organelles complex-1, subunit 3
Alternative Symbols: RP, HPS8, BLOS3
Protein Name: Biogenesis of lysosome-related organelles complex 1 subunit 3
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Poids moléculaire
- 21kDa
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ID gène
- 388552
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NCBI Accession
- NP_997715
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UniProt
- Q6QNY0
Antigène
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