D2HGDH anticorps (N-Term)

N° du produit ABIN2790470

Détail du produit anti-D2HGDH anticorps

Antigène: D2HGDH (D-2-Hydroxyglutarate Dehydrogenase (D2HGDH))

Épitope: N-Term

Reactivité: Humain, Poisson zèbre (Danio rerio), Souris, Rat, Lapin, Chien, Cheval, Boeuf (Vache), Cobaye

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp D2HGDH est non-conjugé

Application: Western Blotting (WB)

Séquence: AFERIVPGGV VTDPEALQAP NVDWLRTLRG CSKVLLRPRT SEEVSHILRH

Homologie: Cow: 79%, Dog: 92%, Guinea Pig: 85%, Horse: 79%, Human: 100%, Mouse: 86%, Rabbit: 92%, Rat: 93%, Zebrafish: 77%

Attributs du produit: This is a rabbit polyclonal antibody against D2HGDH. It was validated on Western Blot.

Purification: Affinity Purified

Immunogène: The immunogen is a synthetic peptide directed towards the N-terminal region of human D2HGDH

Information d'application

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1 mg/mL

Buffer: Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Conseil sur la manipulation: Avoid repeat freeze-thaw cycles.

Stock: -20 °C

Stockage commentaire: For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.

Détails sur D2HGDH

Antigène: D2HGDH (D-2-Hydroxyglutarate Dehydrogenase (D2HGDH))

Autre désignation: D2HGDH (D2HGDH Produits)

Synonymes: anticorps AA408776, anticorps AA408778, anticorps AI325464, anticorps RGD1307976, anticorps D2HGD, anticorps zgc:158661, anticorps D-2-hydroxyglutarate dehydrogenase, anticorps D2hgdh, anticorps D2HGDH, anticorps d2hgdh

Sujet: This gene encodes D-2hydroxyglutarate dehydrogenase, a mitochondrial enzyme belonging to the FAD-binding oxidoreductase/transferase type 4 family. This enzyme, which is most active in liver and kidney but also active in heart and brain, converts D-2-hydroxyglutarate to 2-ketoglutarate. Mutations in this gene are present in D-2-hydroxyglutaric aciduria, a rare recessive neurometabolic disorder causing developmental delay, epilepsy, hypotonia, and dysmorphic features.
Alias Symbols: D2HGD
Protein Size: 325

Poids moléculaire: 35 kDa

ID gène: 728294

NCBI Accession: NM_001287249, NP_001274178

UniProt: Q8N465