L’anticorps anti-Peroxisomal Bifunctional Enzyme Polyclonal produit chez le Lapin a été validé pour WB. Il convient pour la détection de Peroxisomal Bifunctional Enzyme dans des échantillons provenant de Humain.
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This is a rabbit polyclonal antibody against ECHP. It was validated on Western Blot.
Purification
Affinity purified
Immunogène
The immunogen is a synthetic peptide directed towards the middle region of Human ECHP
Indications d'application
Optimal working dilution should be determined by the investigator.
Restrictions
For Research Use only
Format
Liquid
Buffer
Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
Agent conservateur
Sodium azide
Précaution d'utilisation
This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Stock
-20 °C
Stockage commentaire
For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
Antigène
Peroxisomal Bifunctional Enzyme (ECHP)
Autre désignation
ECHP
Sujet
The protein encoded by this gene is a bifunctional enzyme and is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of the encoded protein contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in this gene are a cause of peroxisomal disorders such as Zellweger syndrome. Two transcript variants encoding different isoforms have been found for this gene.