Peroxisomal Bifunctional Enzyme anticorps (Middle Region)
Aperçu rapide pour Peroxisomal Bifunctional Enzyme anticorps (Middle Region) (ABIN5514454)
Antigène
Reactivité
Hôte
Clonalité
Application
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Épitope
- Middle Region
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Séquence
- VIAVDSDKNQ LATANKMITS VLEKEASKMQ QSGHPWSGPK PRLTSSVKEL
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Attributs du produit
- This is a rabbit polyclonal antibody against ECHP. It was validated on Western Blot.
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Purification
- Affinity purified
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Immunogène
- The immunogen is a synthetic peptide directed towards the middle region of Human ECHP
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Indications d'application
- Optimal working dilution should be determined by the investigator.
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Restrictions
- For Research Use only
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Format
- Liquid
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Buffer
- Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
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Agent conservateur
- Sodium azide
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Précaution d'utilisation
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Stock
- -20 °C
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Stockage commentaire
- For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
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- Peroxisomal Bifunctional Enzyme (ECHP)
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Autre désignation
- ECHP
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Sujet
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The protein encoded by this gene is a bifunctional enzyme and is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of the encoded protein contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in this gene are a cause of peroxisomal disorders such as Zellweger syndrome. Two transcript variants encoding different isoforms have been found for this gene.
Alias Symbols: EHHADH, ECHD,
Protein Size: 723 -
ID gène
- 1962
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NCBI Accession
- NP_001957
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UniProt
- Q08426
Antigène
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