PYGM anticorps (C-Term)
Aperçu rapide pour PYGM anticorps (C-Term) (ABIN5531905)
Antigène
Voir toutes PYGM AnticorpsReactivité
Hôte
Clonalité
Conjugué
Application
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Épitope
- AA 698-727, C-Term
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Purification
- This antibody is prepared by Saturated Ammonium Sulfate (SAS) precipitation followed by dialysis
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Immunogène
- This PYGM antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 698-727 amino acids from the C-terminal region of human PYGM.
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Isotype
- Ig Fraction
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Indications d'application
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For WB starting dilution is: 1:1000
For IHC-P starting dilution is: 1:10~50 -
Restrictions
- For Research Use only
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Format
- Liquid
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Concentration
- 2 mg/mL
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Buffer
- Supplied in PBS with 0.09 % (W/V) sodium azide.
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Agent conservateur
- Sodium azide
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Précaution d'utilisation
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Stock
- 4 °C,-20 °C
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Stockage commentaire
- Store at 4°C for three months and -20°C, stable for up to one year. As with all antibodies care should be taken to avoid repeated freeze thaw cycles. Antibodies should not be exposed to prolonged high temperatures.
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- PYGM (Phosphorylase, Glycogen, Muscle (PYGM))
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Autre désignation
- PYGM
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Sujet
- PYGM catalyzes and regulates the breakdown of glycogen to glucose-1-phosphate. Defects in PYGM are the cause of glycogen storage disease type 5 (GSD5), also known as McArdle disease. GSD5 is a metabolic disorder resulting in myopathy characterized by exercise intolerance, cramps, muscle weakness and recurrent myoglobinuria.
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Poids moléculaire
- 97 kDa
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ID gène
- 5837
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UniProt
- P11217
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Pathways
- Cellular Glucan Metabolic Process
Antigène
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