Aminoacylase 1 anticorps (AA 1-408)

N° du produit ABIN5775904

L’anticorps Souris Monoclonal anti-Aminoacylase 1 a été validé pour WB, ELISA, FACS, IF et ICC. Il convient pour détecter Aminoacylase 1 dans des échantillons de Humain.

Aperçu rapide pour Aminoacylase 1 anticorps (AA 1-408) (ABIN5775904)

Antigène: Aminoacylase 1 (ACY1)

Reactivité: Humain

Hôte: Souris

Clonalité: Monoclonal

Conjugué: Cet anticorp Aminoacylase 1 est non-conjugé

Application: Western Blotting (WB), ELISA, Flow Cytometry (FACS), Immunofluorescence (IF), Immunocytochemistry (ICC)

Clone: AT1E2

Détail du produit anti-Aminoacylase 1 anticorps

Épitope: AA 1-408

Immunogène: Recombinant human ACY1 (1-408aa) purified from E. coli

Isotype: IgG2b kappa

Information d'application

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1 mg/mL

Stock: 4 °C,-20 °C,-80 °C

Stockage commentaire: Can be stored at +2°C to +8°C for 1 week. For long term storage, aliquot and store at -20°C to -80°C. Avoid repeated freezing and thawing cycles.

Détails sur Aminoacylase 1

Antigène: Aminoacylase 1 (ACY1)

Autre désignation: Aminoacylase/ACY1

Sujet: Aminoacylase-1, also designated N-acyl-L-amino-acid amidohydrolase or ACY1, is a member of the largest metallopeptidase family called M20A. Aminoacylase-1 is a zinc-binding homodimeric enzyme expressed in kidney, brain, placenta and spleen. It is the most abundant of the aminoacylases. Defects in ACY1 are the cause of aminoacylase-1 deficiency (ACY1D). ACY1D results in a metabolic disorder manifesting with encephalopathy, unspecific psychomotor delay, psychomotor delay with atrophy of the vermis and syringomyelia, marked muscular hypotonia or normal clinical features. All affected individuals exhibit markedly increased urinary excretion of several N-acetylated amino acids.

NCBI Accession: NP_000657