BCKDHA anticorps

N° du produit ABIN6572016

Cet anticorps anti-BCKDHA est un anticorps Lapin Polyclonal détectant BCKDHA dans WB. Adapté pour Humain, Souris et Rat.

Aperçu rapide pour BCKDHA anticorps (ABIN6572016)

Antigène: BCKDHA (Branched Chain Keto Acid Dehydrogenase E1, alpha Polypeptide (BCKDHA))

Reactivité: Humain, Souris, Rat

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp BCKDHA est non-conjugé

Application: Western Blotting (WB)

Détail du produit anti-BCKDHA anticorps

Purification: Affinity purification

Immunogène: Recombinant protein of human BCKDHA

Isotype: IgG

Information d'application

Indications d'application: WB 1:500 - 1:2000

Restrictions: For Research Use only

Stockage

Concentration: 1 mg/mL

Buffer: Buffer: PBS with 0.02 % sodium azide, 50 % glycerol,  pH 7.3.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Store at -20°C. Avoid freeze / thaw cycles.

Détails sur BCKDHA

Antigène: BCKDHA (Branched Chain Keto Acid Dehydrogenase E1, alpha Polypeptide (BCKDHA))

Autre désignation: BCKDHA

Sujet:

Synonyms: Branched chain alpha keto acid dehydrogenase E1 component alpha polypeptide, FLJ45695, OVD1A,2 oxoisovalerate dehydrogenase (lipoamide),2 oxoisovalerate dehydrogenase subunit alpha, mitochondrial ,2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial,BCKDE1A,BCKDH E1 alpha,BCKDH E1-alpha,BCKDHA,Branched chain alpha keto acid dehydrogenase E1 component alpha chain,Branched chain keto acid dehydrogenase E1 alpha polypeptide,Branched chain keto acid dehydrogenase E1, alpha polypeptide (maple syrup urine disease),Branched-chain alpha-keto acid dehydrogenase E1 component alpha chain,MSU,MSUD1,ODBA

Background: The branched-chain alpha-keto acid (BCAA) dehydrogenase (BCKD) complex is an innter mitochondrial enzyme complex that catalyzes the second major step in the catabolism of the branched-chain amino acids leucine, isoleucine, and valine. The BCKD complex consists of three catalytic components: a heterotetrameric (alpha2-beta2) branched-chain alpha-keto acid decarboxylase (E1), a dihydrolipoyl transacylase (E2), and a dihydrolipoamide dehydrogenase (E3). This gene encodes the alpha subunit of the decarboxylase (E1) component. Mutations in this gene result in maple syrup urine disease, type IA. Multiple transcript variants encoding different isoforms have been found for this gene.

Poids moléculaire:

Observed_MW: 50kDa

Calculated_MW: 50kDa

ID gène: 593

UniProt: P12694