ASS1 anticorps
Aperçu rapide pour ASS1 anticorps (ABIN7245992)
Antigène
Voir toutes ASS1 AnticorpsReactivité
Hôte
Clonalité
Conjugué
Application
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Attributs du produit
- Polyclonal Antibody
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Purification
- Antigen affinity purification
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Immunogène
- Fusion protein of human ASS1
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Isotype
- IgG
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Indications d'application
- WB 1:500-1:2000, IHC 1:25-1:100, ELISA 1:5000-1:10000
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Restrictions
- For Research Use only
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Format
- Liquid
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Concentration
- 0.5 mg/mL
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Buffer
- PBS with 0.05 % Sodium azide and 40 % Glycerol, pH 7.4
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Agent conservateur
- Sodium azide
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Précaution d'utilisation
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Stock
- -20 °C
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Stockage commentaire
- Store at -20°C. Avoid freeze / thaw cycles.
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- ASS1 (Argininosuccinate Synthase 1 (ASS1))
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Autre désignation
- ASS1
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Sujet
- ASS1 is a rate-limiting enzyme in the urea cycle. Citrullinemia type I is an autosomal recessive disorder that is caused by a deficiency of the urea cycle enzyme argininosuccinate synthetase (ASS1). Deficiency of ASS1 shows various clinical manifestations encompassing severely affected patients with fatal neonatal hyperammonemia as well as asymptomatic individuals with only a biochemical phenotype.
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Poids moléculaire
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Observed_MW: Refer to figures
Calculated_MW: 47 kDa
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UniProt
- P00966
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Pathways
- Response to Growth Hormone Stimulus, Cellular Response to Molecule of Bacterial Origin
Antigène
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