HMBS anticorps

N° du produit ABIN7252537

Détail du produit anti-HMBS anticorps

Antigène: HMBS (Hydroxymethylbilane Synthase (HMBS))

Reactivité: Humain, Souris, Rat

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp HMBS est non-conjugé

Application: ELISA, Immunohistochemistry (IHC)

Attributs du produit: Polyclonal Antibody

Purification: Antigen affinity purification

Immunogène: Fusion protein of human HMBS

Isotype: IgG

Information d'application

Indications d'application: IHC 1:30-1:150, ELISA 1:5000-1:10000

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 0.78 mg/mL

Buffer: PBS with 0.05 % Sodium azide and 40 % Glycerol, pH 7.4

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Store at -20°C. Avoid freeze / thaw cycles.

Détails sur HMBS

Antigène: HMBS (Hydroxymethylbilane Synthase (HMBS))

Autre désignation: HMBS (HMBS Produits)

Synonymes: anticorps PBG-D, anticorps PBGD, anticorps PORC, anticorps UPS, anticorps URO-S, anticorps hemC, anticorps pbg-d, anticorps pbgd, anticorps ups, anticorps SPAC806.01, anticorps DDBDRAFT_0186148, anticorps DDBDRAFT_0231417, anticorps DDB_0186148, anticorps DDB_0231417, anticorps Hmbs, anticorps NV50236, anticorps T25658, anticorps Ups, anticorps Uros1, anticorps hmbs, anticorps zgc:64128, anticorps hmbsl, anticorps id:ibd5004, anticorps im:7140060, anticorps zgc:110690, anticorps hydroxymethylbilane synthase, anticorps hydroxymethylbilane synthase S homeolog, anticorps hydroxymethylbilane synthase L homeolog, anticorps hydroxymethylbilane synthase (predicted), anticorps Hydroxymethylbilane synthase, anticorps hydroxymethylbilane synthase a, anticorps hydroxymethylbilane synthase, b, anticorps HMBS, anticorps Hmbs, anticorps hmbs, anticorps hmbs.2.S, anticorps hmbs.L, anticorps CNC02250, anticorps hem3, anticorps hemC, anticorps Trad_0335, anticorps Plabr_2100, anticorps Sgly_3113, anticorps SMLT_RS19660, anticorps PMI_RS16580, anticorps hmbsa, anticorps hmbsb

Sujet: This gene encodes a member of the hydroxymethylbilane synthase superfamily. The encoded protein is the third enzyme of the heme biosynthetic pathway and catalyzes the head to tail condensation of four porphobilinogen molecules into the linear hydroxymethylbilane. Mutations in this gene are associated with the autosomal dominant disease acute intermittent porphyria. Alternatively spliced transcript variants encoding different isoforms have been described.

UniProt: P08397