GATM anticorps

N° du produit ABIN7262473

Détail du produit anti-GATM anticorps

Antigène: GATM (Glycine Amidinotransferase (L-Arginine:glycine Amidinotransferase) (GATM))

Reactivité: Humain, Souris, Rat

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp GATM est non-conjugé

Application: Western Blotting (WB), Immunohistochemistry (IHC), Immunofluorescence (IF)

Attributs du produit: Polyclonal Antibody

Purification: Affinity purification

Immunogène: Recombinant fusion protein of human GATM (NP_001473.1).

Isotype: IgG

Information d'application

Indications d'application: WB 1:500-1:2000 IHC 1:50-1:200 IF 1:50-1:200

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1 mg/mL

Buffer: PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Store at -20°C. Avoid freeze / thaw cycles.

Détails sur GATM

Antigène: GATM (Glycine Amidinotransferase (L-Arginine:glycine Amidinotransferase) (GATM))

Autre désignation: GATM (GATM Produits)

Synonymes: anticorps AT, anticorps AGAT, anticorps CCDS3, anticorps 1810003P21Rik, anticorps AI314789, anticorps cb409, anticorps wu:fa08a06, anticorps zgc:65855, anticorps glycine amidinotransferase (L-arginine:glycine amidinotransferase) L homeolog, anticorps glycine amidinotransferase, anticorps glycine amidinotransferase (L-arginine:glycine amidinotransferase), anticorps gatm.L, anticorps GATM, anticorps Gatm, anticorps gatm

Sujet: This gene encodes a mitochondrial enzyme that belongs to the amidinotransferase family. This enzyme is involved in creatine biosynthesis, whereby it catalyzes the transfer of a guanido group from L-arginine to glycine, resulting in guanidinoacetic acid, the immediate precursor of creatine. Mutations in this gene cause arginine:glycine amidinotransferase deficiency, an inborn error of creatine synthesis characterized by mental retardation, language impairment, and behavioral disorders.

Poids moléculaire:

Observed_MW: 43 kDa

Calculated_MW: 44 kDa/48 kDa

ID gène: 2628

UniProt: P50440