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Adenylosuccinate Lyase anticorps

ADSL Reactivité: Humain, Souris, Rat WB, IHC, ELISA, IF, FACS Hôte: Lapin Polyclonal unconjugated
N° du produit ABIN7111349
  • Antigène Voir toutes Adenylosuccinate Lyase (ADSL) Anticorps
    Adenylosuccinate Lyase (ADSL)
    Reactivité
    • 38
    • 20
    • 5
    • 3
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    Humain, Souris, Rat
    Hôte
    • 34
    • 4
    Lapin
    Clonalité
    • 35
    • 2
    Polyclonal
    Conjugué
    • 19
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    Cet anticorp Adenylosuccinate Lyase est non-conjugé
    Application
    • 16
    • 13
    • 13
    • 9
    • 7
    • 6
    • 5
    • 4
    • 3
    • 3
    • 2
    • 2
    • 2
    • 1
    Western Blotting (WB), Immunohistochemistry (IHC), ELISA, Immunofluorescence (IF), Flow Cytometry (FACS)
    Purification
    Immunogen affinity purified
    Pureté
    ≥95 % as determined by SDS-PAGE
    Immunogène
    adenylosuccinate lyase
    Isotype
    IgG
    Top Product
    Discover our top product ADSL Anticorps primaire
  • Indications d'application
    WB: 1:500-1:5000, IHC: 1:20-1:200, IF: 1:10-1:100
    Restrictions
    For Research Use only
  • Format
    Liquid
    Buffer
    PBS with 0.02 % sodium azide and 50 % glycerol pH 7.3,
    Agent conservateur
    Sodium azide
    Précaution d'utilisation
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    Stock
    -20 °C
    Stockage commentaire
    -20°C for 12 months (Avoid repeated freeze / thaw cycles.)
    Date de péremption
    12 months
  • Antigène
    Adenylosuccinate Lyase (ADSL)
    Autre désignation
    Adenylosuccinate lyase (ADSL Produits)
    Synonymes
    anticorps fi60b04, anticorps zgc:56061, anticorps wu:fi60b04, anticorps MGC53383, anticorps MGC69239, anticorps adsL, anticorps F15C21.8, anticorps F15C21_8, anticorps AMPS, anticorps ASASE, anticorps ASL, anticorps Adl, anticorps Asl, anticorps purB, anticorps adenylosuccinate lyase, anticorps adenylosuccinate lyase L homeolog, anticorps adenylosuccinase; ASL, anticorps Adenylosuccinate lyase, anticorps L-Aspartase-like family protein, anticorps ADSL, anticorps adsl, anticorps adsl.L, anticorps ASL, anticorps purB, anticorps purB,adsL, anticorps Mrub_2293, anticorps MMAH_RS02975, anticorps Arnit_0089, anticorps Mesil_1058, anticorps Slip_0597, anticorps Trad_2452, anticorps Deba_0652, anticorps Toce_1174, anticorps Acear_2324, anticorps Igag_0272, anticorps Saut_2156, anticorps Fbal_1996, anticorps Ndas_2434, anticorps Ilyop_0196, anticorps Lbys_2961, anticorps MFER_RS02920, anticorps Palpr_2192, anticorps Calni_0061, anticorps Ftrac_3746, anticorps AT1G36280, anticorps Olsu_1764, anticorps Adsl
    Sujet
    Synonyms:Adenylosuccinase, adenylosuccinate lyase, ADSL, AMPS, ASASE, ASL Background:ADSL(adenylosuccinate lyase) is also named as AMPS, ASase, ASL and belongs to the lyase 1 family. It is an enzyme involved in 2 pathways of purine nucleotide metabolism and catalyzes cleavage of succinyl groups to yield fumarate(PMID:18524658). Defects in ADSL are the cause of adenylosuccinase deficiency(ADSL deficiency). In humans, mutations in ADSL lead to an inborn error of metabolism originally characterized by developmental delay, often with autistic features(PMID:20884265)..The ADSL enzymatic activity is reduced in lymphocytes and red blood cells of the patient with severe psychomotor retardation(PMID:9545543). It has 2 isoforms produced by alternative splicing.
    Poids moléculaire
    55 kDa
    ID gène
    158
    UniProt
    P30566
    Pathways
    Ribonucleoside Biosynthetic Process
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