SGSH anticorps
Aperçu rapide pour SGSH anticorps (ABIN7116690)
Antigène
Voir toutes SGSH AnticorpsReactivité
Hôte
Clonalité
Conjugué
Application
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Fonction
- SGSH antibody
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Purification
- Immunogen affinity purified
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Pureté
- ≥95 % as determined by SDS-PAGE
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Immunogène
- N-sulfoglucosamine sulfohydrolase
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Isotype
- IgG
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Indications d'application
- WB: 1:500 - 1:2000, IHC: 1:50 - 1:100
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Restrictions
- For Research Use only
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Format
- Liquid
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Buffer
- PBS with 0.02 % sodium azide and 50 % glycerol pH 7.3,
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Agent conservateur
- Sodium azide
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Précaution d'utilisation
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Conseil sur la manipulation
- Avoid repeated freeze / thaw cycles.
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Stock
- -20 °C
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Stockage commentaire
- -20°C for 12 months
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Date de péremption
- 12 months
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- SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))
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Autre désignation
- SGSH
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Sujet
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Synonyms: N-sulphoglucosamine sulphohydrolase|Sulfoglucosamine sulfamidase|Sulphamidase|SGSH|HSS
Background: This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.
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Poids moléculaire
- 57 kDa
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ID gène
- 6448
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UniProt
- P51688
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Pathways
- Glycosaminoglycan Metabolic Process
Antigène
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