ACOX1 anticorps (AA 221-320)

N° du produit ABIN708491

L’anticorps anti-ACOX1 Polyclonal Lapin est utilisé pour la détection de ACOX1 dans des échantillons de Humain. Il a été validé pour WB.

Aperçu rapide pour ACOX1 anticorps (AA 221-320) (ABIN708491)

Antigène: ACOX1 (Acyl-CoA Oxidase 1, Palmitoyl (ACOX1))

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp ACOX1 est non-conjugé

Application: Western Blotting (WB)

Détail du produit anti-ACOX1 anticorps

Épitope: AA 221-320

Fonction: ACOX1 Polyclonal Antibody

Réactivité croisée: Humain, Souris, Rat

Homologie: Dog,Cow,Sheep,Horse,Rabbit

Purification: Purified by Protein A.

Immunogène: KLH conjugated synthetic peptide derived from human ACOX1

Isotype: IgG

Information d'application

Indications d'application: WB(1:300-5000),

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1 μg/μL

Buffer: 0.01M TBS( pH 7.4) with 1 % BSA, 0.02 % Proclin300 and 50 % Glycerol.

Agent conservateur: ProClin

Précaution d'utilisation: This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: 4 °C,-20 °C

Stockage commentaire: Shipped at 4C. Store at -20C for one year. Avoid repeated freeze/thaw cycles.

Date de péremption: 12 months

Détails sur ACOX1

Antigène: ACOX1 (Acyl-CoA Oxidase 1, Palmitoyl (ACOX1))

Autre désignation: ACOX1

Sujet:

Synonyms: ACOX1, ACOX1_HUMAN, AOX antibody Palmitoyl CoA oxidase, Palmitoyl-CoA oxidase, Peroxisomal acyl coenzyme A oxidase 1, Peroxisomal acyl-coenzyme A oxidase 1, SCOX, Straight chain acyl CoA oxidase, Straight-chain acyl-CoA oxidase.

Background: Defects in ACOX1 are the cause of adrenoleukodystrophy pseudoneonatal (Pseudo-NALD), also known as peroxisomal acyl-CoA oxidase deficiency. Pseudo-NALD is a peroxisomal single-enzyme disorder. Clinical features include mental retardation, leukodystrophy, seizures, mild hepatomegaly, hearing deficit. Pseudo-NALD is characterized by increased plasma levels of very-long chain fatty cids, due to decreased or absent peroxisome acyl-CoA oxidase activity. Peroxisomes are intact and functioning.

ID gène: 51

Pathways: Regulation of Lipid Metabolism by PPARalpha, Monocarboxylic Acid Catabolic Process