AGA anticorps
Aperçu rapide pour AGA anticorps (ABIN7128282)
Antigène
Voir toutes AGA AnticorpsReactivité
Hôte
Clonalité
Conjugué
Application
-
-
Réactivité croisée
- Humain, Souris, Rat
-
Purification
- Antigen affinity purification
-
Immunogène
- Fusion protein of Human AGA
-
Isotype
- IgG
-
-
-
-
Indications d'application
- ELISA:1:1000-1:2000, WB:1:200-1:1000, IHC:1:15-1:50,
-
Restrictions
- For Research Use only
-
-
-
Format
- Liquid
-
Buffer
- -20 °C, pH 7.4 PBS, 0.05 % Sodium azide, 40 % Glycerol
-
Agent conservateur
- Sodium azide
-
Précaution d'utilisation
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
-
Stock
- -20 °C,-80 °C
-
Stockage commentaire
- Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
-
-
- AGA (Aspartylglucosaminidase (AGA))
-
Autre désignation
- AGA
-
Sujet
-
Background: Aspartylglucosaminidase is involved in the catabolism of N-linked oligosaccharides of glycoproteins. It cleaves asparagine from N-acetylglucosamines as one of the final steps in the lysosomal breakdown of glycoproteins. The lysosomal storage disease aspartylglycosaminuria is caused by a deficiency in the AGA enzyme. Alternatively spliced transcript variants have been identified.
Aliases: Aga antibody, AGU antibody, Aspartylglucosaminidase antibody, Aspartylglucosylamine deaspartylase antibody, Aspartylglycosaminuria antibody, ASPG_HUMAN antibody, ASRG antibody, GA antibody, Glycosylasparaginase antibody, Glycosylasparaginase beta chain antibody, N(4)-(beta-N-acetylglucosaminyl)-L-asparaginase antibody, N4 (N acetyl beta glucosaminyl) L asparagine amidase antibody, N4-(N-acetyl-beta-glucosaminyl)-L-asparagine amidase antibody
-
UniProt
- P20933
Antigène
-