SGSH anticorps (AA 206-502)

N° du produit ABIN7872102

L’anticorps anti-SGSH Polyclonal Lapin est utilisé pour la détection de SGSH dans des échantillons de Humain, Rat et Souris. Il a été validé pour WB, ELISA, IHC (p) et FACS.

Aperçu rapide pour SGSH anticorps (AA 206-502) (ABIN7872102)

Antigène: SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))

Reactivité: Humain, Rat, Souris

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp SGSH est non-conjugé

Application: Western Blotting (WB), ELISA, Immunohistochemistry (Paraffin-embedded Sections) (IHC (p)), Flow Cytometry (FACS)

Détail du produit anti-SGSH anticorps

Épitope: AA 206-502

Fonction: SGSH Antibody / N-sulphoglucosamine sulphohydrolase / HSS

Purification: Antigen affinity purified

Immunogène: E. coli-derived recombinant human protein (amino acids R206-L502) was used as the immunogen for the SGSH antibody.

Isotype: IgG

Information d'application

Indications d'application: Optimal dilution of the SGSH antibody should be determined by the researcher.

Restrictions: For Research Use only

Stockage

Format: Lyophilized

Buffer: 0.5 mg/mL if reconstituted with 0.2 mL sterile DI water

Stock: 4 °C,-20 °C

Stockage commentaire: After reconstitution, the SGSH antibody can be stored for up to one month at 4oC. For long-term, aliquot and store at -20oC. Avoid repeated freezing and thawing.

Détails sur SGSH

Antigène: SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))

Autre désignation: SGSH

Sujet: N-sulphoglucosamine sulphohydrolase is an enzyme that in humans is encoded by the SGSH gene. This gene encodes the enzyme sulfamidase, one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with the lysosomal storage disease mucopolysaccaridosis IIIA, also known as Sanfilippo syndrome A, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.

UniProt: P51688

Pathways: Glycosaminoglycan Metabolic Process