MCCC2 anticorps (AA 204-254)
Aperçu rapide pour MCCC2 anticorps (AA 204-254) (ABIN8122903)
Antigène
Voir toutes MCCC2 AnticorpsReactivité
Hôte
Clonalité
Conjugué
Application
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Épitope
- AA 204-254
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Fonction
- MCCB Antibody
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Specificité
- This antibody detects endogenous levels of MCCB at Human/Mouse/Rat
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Purification
- The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
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Immunogène
- Synthesized peptide derived from human MCCB AA range: 204-254
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Isotype
- IgG
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Indications d'application
- WB 1:500-2000
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Restrictions
- For Research Use only
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Format
- Liquid
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Buffer
- Liquid in PBS containing 50 % glycerol, 0.5 % BSA and 0.02 % sodium azide.
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Agent conservateur
- Sodium azide
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Précaution d'utilisation
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Stock
- -20 °C
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Stockage commentaire
- Store at -20°C/1 year
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Date de péremption
- 12 months
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- MCCC2 (Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2))
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Autre désignation
- MCCB
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Sujet
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Synonyms: Methylcrotonoyl-CoA carboxylase beta chain, mitochondrial (MCCase subunit beta) (EC 6.4.1.4) (3-methylcrotonyl-CoA carboxylase 2) (3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit) (3-methylcrotonyl-CoA:carbon dioxide ligase subunit beta)
Background: This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism. [provided by RefSeq, Jul 2008],
Gene Name: MCCC2 MCCB
Protein Name: MCCB
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ID gène
- 64087
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UniProt
- Q9HCC0
Antigène
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