SGSH anticorps

N° du produit ABIN8123211

L’anticorps anti-SGSH Monoclonal Lapin est utilisé pour la détection de SGSH dans des échantillons de Humain. Il a été validé pour WB, IHC, ICC et IF.

Aperçu rapide pour SGSH anticorps (ABIN8123211)

Antigène: SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))

Reactivité: Humain

Hôte: Lapin

Clonalité: Monoclonal

Conjugué: Cet anticorp SGSH est non-conjugé

Application: Western Blotting (WB), Immunohistochemistry (IHC), Immunocytochemistry (ICC), Immunofluorescence (IF)

Clone: AB2262

Détail du produit anti-SGSH anticorps

Fonction: SGSH Rabbit mAb

Specificité: This antibody detects endogenous levels of SGSH protein.

Purification: The antibody was purified by protein A affinity chromatography.

Immunogène: Recombinant protein (or fragment).

Isotype: IgG

Information d'application

Indications d'application: WB, 1:1000-1:5000 | IHC, 1:100-1:300 | IF, 1:100-1:300 |

Restrictions: For Research Use only

Stockage

Format: Liquid

Buffer: The antibody is provided in liquid form in phosphate - buffered saline with 50 % glycerol, 0.05 % BSA, and 0.05 % Proclin 300.

Agent conservateur: ProClin

Précaution d'utilisation: This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Conseil sur la manipulation: Avoid freeze / thaw cycles

Stock: -20 °C

Stockage commentaire: Store at-20°C. Avoid freeze / thaw cycles.

Détails sur SGSH

Antigène: SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))

Autre désignation: SGSH

Sujet:

Synonyms: SGSH, HSS, N-sulphoglucosamine sulphohydrolase , Sulfoglucosamine sulfamidase, Sulphamidase,

Background: This gene encodes the enzyme sulfamidase, one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with the lysosomal storage disease mucopolysaccaridosis IIIA, also known as Sanfilippo syndrome A, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. [provided by RefSeq, Jun 2017]

Gene Name: SGSH, HSS

Protein Name: SGSH

ID gène: 6448

UniProt: P51688

Pathways: Glycosaminoglycan Metabolic Process