SGSH anticorps (C-Term)

N° du produit ABIN954998

Détail du produit anti-SGSH anticorps

Antigène: SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))

Épitope: AA 427-457, C-Term

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp SGSH est non-conjugé

Application: Western Blotting (WB), Enzyme Immunoassay (EIA)

Specificité: Recognizes Sulphamidase / SGSH (C-term).

Purification: Protein A column followed by peptide Affinity purification

Immunogène: KLH conjugated synthetic peptide between 427~457 amino acids from the C-terminal region of Human SGSH. Genename: SGSH

Isotype: Ig Fraction

Information d'application

Indications d'application: Optimal working dilution should be determined by the investigator.

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 0.25 mg/mL

Buffer: PBS with 0.09 % (W/V) Sodium Azide as preservative

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Conseil sur la manipulation: Avoid repeated freezing and thawing.

Stock: 4 °C/-20 °C

Stockage commentaire: Store the antibody undiluted at 2-8 °C for one month or (in aliquots) at -20 °C for longer.

Détails sur SGSH

Antigène: SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))

Autre désignation: Sulphamidase / SGSH (SGSH Produits)

Synonymes: anticorps HSS, anticorps MPS3A, anticorps SFMD, anticorps 4632406A19Rik, anticorps N-sulfoglucosamine sulfohydrolase, anticorps N-sulfoglucosamine sulfohydrolase (sulfamidase), anticorps SGSH, anticorps Sgsh

Sujet: SGSH is one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.Synonyms: HSS, N-sulphoglucosamine sulphohydrolase, Sulfoglucosamine sulfamidase

ID gène: 6448

NCBI Accession: NP_000190

Pathways: Glycosaminoglycan Metabolic Process