Glucosidase, Alpha, Acid (GAA) Peptide
GAA
Reactivité: Mammifères
Hôte: Synthetic
BP, IHC, WB
N° du produit ABIN938303
Aperçu rapide pour Glucosidase, Alpha, Acid (GAA) Peptide (ABIN938303)
Antigène
GAA
(Glucosidase, Alpha, Acid (GAA))
Origine
Mammifères
Source
Synthetic
Application
Blocking Peptide (BP), Immunohistochemistry (IHC), Western Blotting (WB)
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Type de proteíne
- Synthetic
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Séquence
- FGVIVRRQLD GRVLLNTTVA PLFFADQFLQ LSTSLPSQYI TGLAEHLSPL
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Attributs du produit
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A synthetic peptide for use as a blocking control in assays to test for specificity of GAA antibody,
Alternative Names: GAA control peptide, GAA antibody Blocking Peptide, Anti-GAA Blocking Peptide, Glucosidase Alpha, Acid Blocking Peptide, LYAG Blocking Peptide
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Indications d'application
- Optimal conditions should be determined by the investigator
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Restrictions
- For Research Use only
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Format
- Lyophilized
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Reconstitution
- Add 100 µL of distilled water for a final peptide concentration is 1 mg/mL.
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Buffer
- PBS
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Conseil sur la manipulation
- Avoid repeated freeze/thaw cycles.
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Stock
- -20 °C
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Stockage commentaire
- Store at -20 °C long term.
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- GAA (Glucosidase, Alpha, Acid (GAA))
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Sujet
- GAA is acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum.
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Poids moléculaire
- 98 kDa
Antigène
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