PPT1 Produits
(Palmitoyl-Protein Thioesterase 1 (PPT1))
Catégories
The protein encoded by this gene is a small glycoprotein involved in the catabolism of lipid-modified proteins during lysosomal degradation. The encoded enzyme removes thioester-linked fatty acyl groups such as palmitate from cysteine residues. Defects in this gene are a cause of infantile neuronal ceroid lipofuscinosis 1 (CLN1, or INCL) and neuronal ceroid lipofuscinosis 4 (CLN4). Two transcript variants encoding different isoforms have been found for this gene.[provided by RefSeq, Dec 2008].
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Catégories PPT1 en vedette
PPT1 Anticorps
High quality antibodies with extensive validation data.
PPT1 Kits ELISA
Reliable ELISA kits for a wide range of species.
PPT1 Protéines
Proteins for various applications incl. WB, ELISA, IF etc.
PPT1 recommandé Anticorps
Produit
Reactivity
Application
Validations
N° du produit
Quantité
Fiche technique
Reactivity
Human
Application
WB, IHC (p), FACS
Validations
- (3)
- (5)
N° du produit
ABIN1944801
Quantité
400 μL
Fiche technique
Fiche technique
Reactivity
Human
Application
WB, IHC, IHC (p)
Validations
- (7)
N° du produit
ABIN1490802
Quantité
100 μL
Fiche technique
Fiche technique
Reactivity
Human
Application
WB, IHC (p)
Validations
- (3)
N° du produit
ABIN389117
Quantité
400 μL
Fiche technique
Fiche technique
PPT1 recommandé Kits ELISA
Produit
Reactivity
Analytical Method
Validations
N° du produit
Quantité
Fiche technique
Reactivity
Human
Analytical Method
Quantitative Sandwich ELISA
Validations
N° du produit
ABIN6951472
Quantité
96 tests
Fiche technique
Fiche technique
Reactivity
Mouse
Analytical Method
Validations
N° du produit
ABIN1146898
Quantité
96 tests
Fiche technique
Fiche technique
Reactivity
Rat
Analytical Method
Validations
N° du produit
ABIN1146899
Quantité
96 tests
Fiche technique
Fiche technique
PPT1 recommandé Protéines
Produit
Reactivity
Source
Validations
N° du produit
Quantité
Fiche technique
Reactivity
Human
Source
Wheat germ
Validations
- (1)
N° du produit
ABIN1316094
Quantité
10 μg
Fiche technique
Fiche technique
Reactivity
Human
Source
Insect Cells
Validations
- (1)
N° du produit
ABIN3086501
Quantité
1 mg
Fiche technique
Fiche technique
Reactivity
Mouse
Source
Insect Cells
Validations
- (1)
N° du produit
ABIN3132137
Quantité
1 mg
Fiche technique
Fiche technique
Dernières publications sur nos produits PPT1
: "Neural stem cells for disease modeling and evaluation of therapeutics for infantile (CLN1/PPT1) and late infantile (CLN2/TPP1) neuronal ceroid lipofuscinoses." dans: Orphanet journal of rare diseases, Vol. 13, Issue 1, pp. 54, (2019) (PubMed).: "Reversible Cysteine Acylation Regulates the Activity of Human Palmitoyl-Protein Thioesterase 1 (PPT1)." dans: PLoS ONE, Vol. 11, Issue 1, pp. e0146466, (2016) (PubMed).
: "Quantitative analysis of PPT1 interactome in human neuroblastoma cells." dans: Data in brief, Vol. 4, pp. 207-16, (2015) (PubMed).
: "The role of ceroid lipofuscinosis neuronal protein 5 (CLN5) in endosomal sorting." dans: Molecular and cellular biology, Vol. 32, Issue 10, pp. 1855-66, (2012) (PubMed).
: "The crystal structure of palmitoyl protein thioesterase-2 (PPT2) reveals the basis for divergent substrate specificities of the two lysosomal thioesterases, PPT1 and PPT2." dans: The Journal of biological chemistry, Vol. 278, Issue 39, pp. 37957-64, (2003) (PubMed).
: "The neuronal ceroid lipofuscinoses: mutations in different proteins result in similar disease." dans: Neuromolecular medicine, Vol. 1, Issue 2, pp. 111-24, (2002) (PubMed).
: "Neuronal ceroid lipofuscinoses caused by defects in soluble lysosomal enzymes (CLN1 and CLN2)." dans: Current molecular medicine, Vol. 2, Issue 5, pp. 423-37, (2002) (PubMed).
: "Didemnin binds to the protein palmitoyl thioesterase responsible for infantile neuronal ceroid lipofuscinosis." dans: Proceedings of the National Academy of Sciences of the United States of America, Vol. 93, Issue 9, pp. 4316-9, (1996) (PubMed).
: "cDNA and genomic cloning of human palmitoyl-protein thioesterase (PPT), the enzyme defective in infantile neuronal ceroid lipofuscinosis." dans: Genomics, Vol. 34, Issue 3, pp. 317-22, (1996) (PubMed).
: "Mutations in the palmitoyl protein thioesterase gene causing infantile neuronal ceroid lipofuscinosis." dans: Nature, Vol. 376, Issue 6541, pp. 584-7, (1995) (PubMed).
Synonymes et noms alternatifs relatifs à PPT1
palmitoyl-protein thioesterase 1 (PPT1), palmitoyl-protein thioesterase 1 (MGYG_00692), palmitoyl-protein thioesterase 1 (Ppt1), Palmitoyl-protein thioesterase 1 (ppt-1), palmitoyl-protein thioesterase 1 (ceroid-lipofuscinosis, neuronal 1, infantile) (ppt1), palmitoyl-protein thioesterase 1 L homeolog (ppt1.L), 9530043G02Rik, AA960502, C77813, CLN1, D4Ertd184e, INCL, PPT, Ppt, PPT-1, ppt1, wu:fj17f04, zgc:63969Protein level used designations for PPT1
- ceroid-palmitoyl-palmitoyl-protein thioesterase 1
- palmitoyl-protein hydrolase 1
- palmitoyl-protein thioesterase 1
- PPT-1
- palmitoyl-protein thioesterase 1 (ceroid-lipofuscinosis, neuronal 1, infantile)
- palmitoyl protein thioesterase
- Palmitoyl-protein hydrolase 1
- palmitoyl-protein thioesterase 1 L homeolog
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