PEX19 anticorps (AA 219-268)
Aperçu rapide pour PEX19 anticorps (AA 219-268) (ABIN1535148)
Antigène
Voir toutes PEX19 AnticorpsReactivité
Hôte
Clonalité
Conjugué
Application
-
-
Épitope
- AA 219-268
-
Fonction
- Peroxin 19 Antibody
-
Specificité
- Peroxin 19 Polyclonal Antibody detects endogenous levels of Peroxin 19 protein.
-
Purification
- The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
-
Pureté
- > 95 %
-
Immunogène
- The antiserum was produced against synthesized peptide derived from human PEX19. AA range:219-268
-
Isotype
- IgG
-
-
-
-
Indications d'application
- WB 1:500 - 1:2000. IHC 1:100 - 1:300. ELISA: 1:5000.. IF 1:50-200
-
Restrictions
- For Research Use only
-
-
-
Format
- Liquid
-
Concentration
- 1 mg/mL
-
Buffer
- Liquid in PBS containing 50 % glycerol, 0.5 % BSA and 0.02 % sodium azide.
-
Agent conservateur
- Sodium azide
-
Précaution d'utilisation
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
-
Stock
- -20 °C
-
Stockage commentaire
- Store at -20°C/1 year
-
Date de péremption
- 12 months
-
-
- PEX19 (Peroxisomal Biogenesis Factor 19 (PEX19))
-
Autre désignation
- PEX19
-
Sujet
-
Synonyms: PEX19, HK33, PXF, OK/SW-cl.22, Peroxisomal biogenesis factor 19, 33 kDa housekeeping protein, Peroxin-19, Peroxisomal farnesylated protein
Background: peroxisomal biogenesis factor 19(PEX19) Homo sapiens This gene is necessary for early peroxisomal biogenesis. It acts both as a cytosolic chaperone and as an import receptor for peroxisomal membrane proteins (PMPs). Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. These disorders have at least 14 complementation groups, with more than one phenotype being observed for some complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of Zellweger syndrome (ZWS), as well as peroxisome biogenesis disorder complementation group 14 (PBD-CG14), which is
Gene Name: PEX19
Protein Name: Peroxisomal biogenesis factor 19
-
Poids moléculaire
- 32 kDa
-
ID gène
- 5824
-
OMIM
- 214100
-
UniProt
- P40855
Antigène
-