DBT anticorps
Aperçu rapide pour DBT anticorps (ABIN2719239)
Antigène
Voir toutes DBT AnticorpsReactivité
Hôte
Clonalité
Conjugué
Application
Clone
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Attributs du produit
- Homo sapiens dihydrolipoamide branched chain transacylase E2 (DBT), nuclear gene encoding mitochondrial protein
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Purification
- Purified from mouse ascites fluids by affinity chromatography
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Immunogène
- Full length human recombinant protein of human DBT(NP_001909) produced in HEK293T cell.
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Isotype
- IgG1
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Indications d'application
- WB 1:2000, FLOW 1:100,
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Commentaires
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The concentration of the product may vary between diferrent lots.
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Restrictions
- For Research Use only
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Format
- Liquid
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Concentration
- 0.5-1.0 mg/mL
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Buffer
- PBS (PH 7.3) containing 1 % BSA, 50 % glycerol and 0.02 % sodium azide.
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Agent conservateur
- Sodium azide
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Précaution d'utilisation
- This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Stock
- -20 °C
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- DBT (Dihydrolipoamide Branched Chain Transacylase E2 (DBT))
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Autre désignation
- DBT
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Sujet
- The branched-chain alpha-keto acid dehydrogenase complex (BCKD) is an inner-mitochondrial enzyme complex involved in the breakdown of the branched-chain amino acids isoleucine, leucine, and valine. The BCKD complex is thought to be composed of a core of 24 transacylase (E2) subunits, and associated decarboxylase (E1), dehydrogenase (E3), and regulatory subunits. This gene encodes the transacylase (E2) subunit. Mutations in this gene result in maple syrup urine disease, type 2. Alternatively spliced transcript variants have been described, but their biological validity has not been determined.
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Poids moléculaire
- 46.4 kDa
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ID gène
- 1629
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NCBI Accession
- NM_001918
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HGNC
- 1629
Antigène
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