PEX19 anticorps (C-Term)

N° du produit ABIN2788834

Détail du produit anti-PEX19 anticorps

Antigène: PEX19 (Peroxisomal Biogenesis Factor 19 (PEX19))

Épitope: C-Term

Reactivité: Humain, Souris, Rat, Lapin, Boeuf (Vache), Chien, Cobaye, Cheval, Porc

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp PEX19 est non-conjugé

Application: Western Blotting (WB)

Séquence: AETPTDSETT QKARFEMVLD LMQQLQDLGH PPKELAGEMP PGLNFDLDAL

Homologie: Cow: 93%, Dog: 93%, Guinea Pig: 86%, Horse: 93%, Human: 100%, Mouse: 86%, Pig: 93%, Rabbit: 86%, Rat: 86%

Attributs du produit: This is a rabbit polyclonal antibody against PEX19. It was validated on Western Blot.

Purification: Affinity Purified

Information d'application

Indications d'application: Optimal working dilutions should be determined experimentally by the investigator.

Commentaires:

Antigen size: 299 AA

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: Lot specific

Buffer: Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Conseil sur la manipulation: Avoid repeated freeze-thaw cycles.

Stock: -20 °C

Stockage commentaire: For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.

Détails sur PEX19

Antigène: PEX19 (Peroxisomal Biogenesis Factor 19 (PEX19))

Autre désignation: PEX19 (PEX19 Produits)

Synonymes: anticorps BEST:GH03076, anticorps CG5325, anticorps DmelPex19, anticorps Dmel\\CG5325, anticorps D1S2223E, anticorps HK33, anticorps PBD12A, anticorps PMP1, anticorps PMPI, anticorps PXF, anticorps PXMP1, anticorps Pxf, anticorps PxF, anticorps Peroxin-19, anticorps Peroxin 19, anticorps Peroxisomal farnesylated protein, anticorps peroxisomal biogenesis factor 19, anticorps Pex19, anticorps Bm1_19905, anticorps PEX19

Sujet: This gene is necessary for early peroxisomal biogenesis. It acts both as a cytosolic chaperone and as an import receptor for peroxisomal membrane proteins (PMPs). Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. These disorders have at least 14 complementation groups, with more than one phenotype being observed for some complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of Zellweger syndrome (ZWS), as well as peroxisome biogenesis disorder complementation group 14 (PBD-CG14), which is also known as PBD-CGJ. Alternative splicing results in multiple transcript variants.
Alias Symbols: D1S2223E, FLJ55296, HK33, PMP1, PMPI, PXF, PXMP1
Protein Interaction Partner: FKBP7, IL23A, PEX3, UBC, PPIB, PTPLAD1, VCP, PXMP4, SLC25A17, PEX16, PEX11B, ABCD3, PMP22, EGFR, Cdkn2a, Pxmp2, TMEM54, MFSD5, PEX26, GSKIP, F11R, KIFAP3, OIP5, EIF1B, PEX11A, STK3, SRPK1, PEX14, PEX13, SMAD2, IRF3, CDC25A, NUDCD2, DSTN, NUBP2, HSPB1, PEX
Protein Size: 299

Poids moléculaire: 33 kDa

ID gène: 5824

NCBI Accession: NM_002857, NP_002848

UniProt: P40855