IDUA anticorps (Middle Region)

N° du produit ABIN2789574

Cet anticorps Lapin Polyclonal détecte spécifiquement IDUA dans WB. Il présente une réactivité envers Humain, Souris, Rat, Cobaye, Cheval, Boeuf (Vache) et Chien.

Aperçu rapide pour IDUA anticorps (Middle Region) (ABIN2789574)

Antigène: IDUA (Iduronidase, alpha-L- (IDUA))

Reactivité: Humain, Souris, Rat, Cobaye, Cheval, Boeuf (Vache), Chien

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp IDUA est non-conjugé

Application: Western Blotting (WB)

Détail du produit anti-IDUA anticorps

Épitope: Middle Region

Séquence: MENQLLPGFE LMGSPSGYFT DFDDKQQVFE WKDLVSLLAR RYIGRYGLTH

Homologie: Cow: 86%, Dog: 90%, Guinea Pig: 100%, Horse: 100%, Human: 100%, Mouse: 86%, Rat: 93%

Attributs du produit: This is a rabbit polyclonal antibody against Idua. It was validated on Western Blot.

Purification: Affinity Purified

Immunogène: The immunogen is a synthetic peptide directed towards the middle region of mouse IDUA

Information d'application

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1 mg/mL

Buffer: Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Conseil sur la manipulation: Avoid repeat freeze-thaw cycles.

Stock: -20 °C

Stockage commentaire: For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.

Détails sur IDUA

Antigène: IDUA (Iduronidase, alpha-L- (IDUA))

Autre désignation: Idua

Sujet: This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I).
Alias Symbols: IDA, MPS1
Protein Size: 281

Poids moléculaire: 30 kDa

ID gène: 3425

NCBI Accession: NM_000203, NP_000194

UniProt: P35475

Pathways: Glycosaminoglycan Metabolic Process