IDUA anticorps (Middle Region)

N° du produit ABIN2789574

Détail du produit anti-IDUA anticorps

Antigène: IDUA (Iduronidase, alpha-L- (IDUA))

Épitope: Middle Region

Reactivité: Humain, Souris, Rat, Cobaye, Cheval, Boeuf (Vache), Chien

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp IDUA est non-conjugé

Application: Western Blotting (WB)

Séquence: MENQLLPGFE LMGSPSGYFT DFDDKQQVFE WKDLVSLLAR RYIGRYGLTH

Homologie: Cow: 86%, Dog: 90%, Guinea Pig: 100%, Horse: 100%, Human: 100%, Mouse: 86%, Rat: 93%

Attributs du produit: This is a rabbit polyclonal antibody against Idua. It was validated on Western Blot.

Purification: Affinity Purified

Immunogène: The immunogen is a synthetic peptide directed towards the middle region of mouse IDUA

Information d'application

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1 mg/mL

Buffer: Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Conseil sur la manipulation: Avoid repeat freeze-thaw cycles.

Stock: -20 °C

Stockage commentaire: For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.

Détails sur IDUA

Antigène: IDUA (Iduronidase, alpha-L- (IDUA))

Autre désignation: Idua (IDUA Produits)

Synonymes: anticorps IDA, anticorps MPS1, anticorps 6030426D08, anticorps alpha-L-iduronidase, anticorps MGC80842, anticorps si:ch211-12e13.9, anticorps IDUA, anticorps iduronidase, alpha-L-, anticorps iduronidase, alpha-L- L homeolog, anticorps alpha-L-iduronidase, anticorps IDUA, anticorps Idua, anticorps idua.L, anticorps idua, anticorps LOC5564727

Sujet: This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I).
Alias Symbols: IDA, MPS1
Protein Size: 281

Poids moléculaire: 30 kDa

ID gène: 3425

NCBI Accession: NM_000203, NP_000194

UniProt: P35475

Pathways: Glycosaminoglycan Metabolic Process