HGSNAT anticorps (C-Term)

N° du produit ABIN2790258

Cet anticorps Lapin Polyclonal détecte spécifiquement HGSNAT dans WB. Il présente une réactivité envers Humain, Souris, Chien, Cheval, Boeuf (Vache), Cobaye, Lapin et Rat.

Aperçu rapide pour HGSNAT anticorps (C-Term) (ABIN2790258)

Antigène: HGSNAT (Heparan-alpha-Glucosaminide N-Acetyltransferase (HGSNAT))

Reactivité: Humain, Souris, Chien, Cheval, Boeuf (Vache), Cobaye, Lapin, Rat

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp HGSNAT est non-conjugé

Application: Western Blotting (WB)

Détail du produit anti-HGSNAT anticorps

Épitope: C-Term

Séquence: VKGLWTGTPF FYPGMNSILV YVGHEVFENY FPFQWKLKDN QSHKEHLTQN

Homologie: Cow: 86%, Dog: 93%, Guinea Pig: 93%, Horse: 79%, Human: 100%, Mouse: 86%, Rabbit: 86%, Rat: 86%

Attributs du produit: This is a rabbit polyclonal antibody against HGSNAT. It was validated on Western Blot.

Purification: Affinity Purified

Immunogène: The immunogen is a synthetic peptide directed towards the C-terminal region of Human HGSNAT

Information d'application

Indications d'application: Optimal working dilutions should be determined experimentally by the investigator.

Commentaires:

Antigen size: 635 AA

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: Lot specific

Buffer: Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Conseil sur la manipulation: Avoid repeated freeze-thaw cycles.

Stock: -20 °C

Stockage commentaire: For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.

Détails sur HGSNAT

Antigène: HGSNAT (Heparan-alpha-Glucosaminide N-Acetyltransferase (HGSNAT))

Autre désignation: HGSNAT

Sujet: This gene encodes a lysosomal acetyltransferase, which is one of several enzymes involved in the lysosomal degradation of heparin sulfate. Mutations in this gene are associated with Sanfilippo syndrome C, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate.
Alias Symbols: DKFZp686G24175, FLJ22242, FLJ32731, HGNAT, MPS3C, TMEM76
Protein Size: 635

Poids moléculaire: 2 kDa

ID gène: 138050

NCBI Accession: NM_152419, NP_689632

UniProt: Q68CP4

Pathways: Glycosaminoglycan Metabolic Process