HGSNAT anticorps (N-Term)

N° du produit ABIN2790259

Cet anticorps anti-HGSNAT Polyclonal Lapin (ABIN2790259) détecte spécifiquement HGSNAT dans WB. L’anticorps est réactif avec des échantillons de Humain, Chien et Cheval.

Aperçu rapide pour HGSNAT anticorps (N-Term) (ABIN2790259)

Antigène: HGSNAT (Heparan-alpha-Glucosaminide N-Acetyltransferase (HGSNAT))

Reactivité: Humain, Chien, Cheval

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp HGSNAT est non-conjugé

Application: Western Blotting (WB)

Détail du produit anti-HGSNAT anticorps

Épitope: N-Term

Fonction: HGSNAT Antibody - N-terminal region

Séquence: RALAALLLAA SVLSAALLAP GGSSGRDAQA APPRDLDKKR HAELKMDQAL

Homologie: Dog: 86%, Horse: 82%, Human: 100%

Attributs du produit: This is a rabbit polyclonal antibody against HGSNAT. It was validated on Western Blot.

Purification: Affinity Purified

Immunogène: The immunogen is a synthetic peptide directed towards the N-terminal region of Human HGSNAT

Information d'application

Indications d'application: Optimal working dilution should be determined by the investigator.

Commentaires:

We also sell a specific blocking peptide that can be used in combination with this antibody. You can find the blocking peptide under AAP65768-100UG

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 0.5 mg/mL

Buffer: Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Conseil sur la manipulation: prevent freeze-thaw cycles

Stock: 4 °C,-20 °C

Stockage commentaire: For short term use, store at 2-8C up to 1 week. For long term storage, store at -20 °C in small aliquots to prevent freeze-thaw cycles.

Détails sur HGSNAT

Antigène: HGSNAT (Heparan-alpha-Glucosaminide N-Acetyltransferase (HGSNAT))

Autre désignation: HGSNAT

Sujet:

Background Information: This gene encodes a lysosomal acetyltransferase, which is one of several enzymes involved in the lysosomal degradation of heparin sulfate. Mutations in this gene are associated with Sanfilippo syndrome C, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate.

Gene Name: heparan-alpha-glucosaminide N-acetyltransferase

Alternative Symbols: RP73, HGNAT, MPS3C, TMEM76

Protein Name: HGSNAT protein EMBL AAH42037.1

Poids moléculaire: 24kDa

ID gène: 138050

UniProt: Q8IVU6

Pathways: Glycosaminoglycan Metabolic Process