HGSNAT anticorps (C-Term)
Aperçu rapide pour HGSNAT anticorps (C-Term) (ABIN2790258)
Antigène
Voir toutes HGSNAT AnticorpsReactivité
Hôte
Clonalité
Conjugué
Application
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Épitope
- C-Term
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Fonction
- HGSNAT Antibody - C-terminal region
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Séquence
- VKGLWTGTPF FYPGMNSILV YVGHEVFENY FPFQWKLKDN QSHKEHLTQN
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Homologie
- Cow: 86%, Dog: 93%, Guinea Pig: 93%, Horse: 79%, Human: 100%, Mouse: 86%, Rabbit: 86%, Rat: 86%
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Attributs du produit
- This is a rabbit polyclonal antibody against HGSNAT. It was validated on Western Blot.
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Purification
- Affinity Purified
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Immunogène
- The immunogen is a synthetic peptide directed towards the C-terminal region of Human HGSNAT
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Indications d'application
- Optimal working dilution should be determined by the investigator.
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Commentaires
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We also sell a specific blocking peptide that can be used in combination with this antibody. You can find the blocking peptide under AAP65767-100UG
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Restrictions
- For Research Use only
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Format
- Liquid
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Concentration
- 0.5 mg/mL
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Buffer
- Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
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Agent conservateur
- Sodium azide
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Précaution d'utilisation
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Conseil sur la manipulation
- prevent freeze-thaw cycles
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Stock
- 4 °C,-20 °C
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Stockage commentaire
- For short term use, store at 2-8C up to 1 week. For long term storage, store at -20 °C in small aliquots to prevent freeze-thaw cycles.
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- HGSNAT (Heparan-alpha-Glucosaminide N-Acetyltransferase (HGSNAT))
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Autre désignation
- HGSNAT
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Sujet
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Background Information: This gene encodes a lysosomal acetyltransferase, which is one of several enzymes involved in the lysosomal degradation of heparin sulfate. Mutations in this gene are associated with Sanfilippo syndrome C, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate.
Alternative Symbols: RP73, HGNAT, MPS3C, TMEM76
Protein Name: Heparan-alpha-glucosaminide N-acetyltransferase
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Poids moléculaire
- 2kDa
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ID gène
- 138050
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NCBI Accession
- NP_689632
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UniProt
- Q68CP4
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Pathways
- Glycosaminoglycan Metabolic Process
Antigène
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