GALNS anticorps (Center)

N° du produit ABIN2856743

Détail du produit anti-GALNS anticorps

Antigène: GALNS (Galactosamine (N-Acetyl)-6-Sulfate Sulfatase (GALNS))

Épitope: Center

Reactivité: Humain, Souris, Rat

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp GALNS est non-conjugé

Application: Western Blotting (WB), Immunofluorescence (IF), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p)), Immunocytochemistry (ICC)

Attributs du produit: Rabbit Polyclonal antibody to GALNS (galactosamine (N-acetyl)-6-sulfate sulfatase)
GALNS antibody

Purification: Purified by antigen-affinity chromatography.

Immunogène: Recombinant protein encompassing a sequence within the center region of human GALNS. The exact sequence is proprietary.

Isotype: IgG

Information d'application

Indications d'application: Suggested dilution Reference ICC/IF 1:100-1:1000* IHC (Formalin-fixed paraffin-embedded sections) 1:100-1:1000* Western blot 1:500-1:3000* Not tested in other applications. *Optimal dilutions/concentrations should be determined by the researcher.Suggested dilutionReferenceICC/IF1:100-1:1000* IHC (Formalin-fixed paraffin-embedded sections)1:100-1:1000* Western blot1:500-1:3000*

Commentaires:

Positive Control: H1299 , Neuro2A , C2C12 , PC-12 , Rat2

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1 mg/mL

Buffer: 0.1M Tris, 0.1M Glycine, 10 % Glycerol ( pH 7). 0.01 % Thimerosal was added as a preservative.

Agent conservateur: Thimerosal (Merthiolate)

Précaution d'utilisation: This product contains Thimerosal (Merthiolate): a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Keep as concentrated solution. Aliquot and store at -20°C or below. Avoid multiple freeze-thaw cycles.

Détails sur GALNS

Antigène: GALNS (Galactosamine (N-Acetyl)-6-Sulfate Sulfatase (GALNS))

Autre désignation: GALNS (GALNS Produits)

Synonymes: anticorps GALNAC6S, anticorps GAS, anticorps GalN6S, anticorps MPS4A, anticorps mFLJ00319, anticorps galns, anticorps zgc:158385, anticorps galactosamine (N-acetyl)-6-sulfatase, anticorps galactosamine (N-acetyl)-6-sulfate sulfatase, anticorps N-acetylgalactosamine-6-sulfatase, anticorps galactosamine (N-acetyl)-6-sulfatase L homeolog, anticorps GALNS, anticorps Galns, anticorps Celly_0425, anticorps galns.L, anticorps galns

Sujet: This gene encodes N-acetylgalactosamine-6-sulfatase which is a lysosomal exohydrolase required for the degradation of the glycosaminoglycans, keratan sulfate, and chondroitin 6-sulfate. Sequence alterations including point, missense and nonsense mutations, as well as those that affect splicing, result in a deficiency of this enzyme. Deficiencies of this enzyme lead to Morquio A syndrome, a lysosomal storage disorder.

Cellular Localization: Lysosome

Poids moléculaire: 58 kDa

ID gène: 2588

Pathways: Glycosaminoglycan Metabolic Process