GLA anticorps (N-Term)

N° du produit ABIN453055

Détail du produit anti-GLA anticorps

Antigène: GLA (Galactosidase, alpha (GLA))

Épitope: AA 90-120, N-Term

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp GLA est non-conjugé

Application: Western Blotting (WB), Enzyme Immunoassay (EIA)

Specificité: This antibody detects GLA at N-term.

Purification: Saturated Ammonium Sulfate (SAS) precipitation followed by dialysis against PBS

Immunogène: KLH conjugated synthetic peptide between 90~120 amino acids from the N-terminal region of human GLA

Information d'application

Indications d'application: Western blot: 1: 50 - 1: 100. ELISA: 1: 1,000.
Other applications not tested.
Optimal dilutions are dependent on conditions and should be determined by the user.

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 0.25 mg/mL

Buffer: PBS with 0.09 % (W/V) sodium azide as preservative

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Conseil sur la manipulation: Avoid repeated freezing and thawing.

Stock: 4 °C/-20 °C

Stockage commentaire: Store the antibody at 2 - 8 °C up to one month or (in aliquots) at -20 °C for longer.

Détails sur GLA

Antigène: GLA (Galactosidase, alpha (GLA))

Autre désignation: alpha-Galactosidase A (GLA Produits)

Synonymes: anticorps GALA, anticorps Ags, anticorps zgc:101584, anticorps MGC130872, anticorps SMU.877, anticorps SCF11.21, anticorps AO090005000217, anticorps alpha-GAL, anticorps galactosidase alpha, anticorps galactosidase, alpha, anticorps galactosidase alpha S homeolog, anticorps alpha-galactosidase, anticorps aga, anticorps alpha-galactosidase A, anticorps GLA, anticorps Gla, anticorps gla, anticorps gla.S, anticorps agaN, anticorps aga, anticorps agaL, anticorps SCO0541, anticorps rafA, anticorps melA, anticorps galA, anticorps ANI_1_2528074, anticorps ANI_1_1502124, anticorps AOR_1_390174, anticorps CpipJ_CPIJ002066, anticorps MCYG_00962, anticorps MCYG_00791, anticorps Tsp_02909, anticorps Tsp_02508

Sujet: GLA is a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties.Synonyms: Alpha-D-galactosidase A, Alpha-D-galactoside galactohydrolase, GLA, Melibiase

Poids moléculaire: 48767 Da

ID gène: 2717

NCBI Accession: NP_000160

UniProt: P06280

Pathways: SARS-CoV-2 Protein Interactome