NAGLU anticorps (C-Term)

N° du produit ABIN5517086

Cet anticorps anti-NAGLU Polyclonal Lapin (ABIN5517086) détecte spécifiquement NAGLU dans WB. L’anticorps est réactif avec des échantillons de Humain.

Aperçu rapide pour NAGLU anticorps (C-Term) (ABIN5517086)

Antigène: NAGLU (N-Acetylglucosaminidase, alpha (NAGLU))

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp NAGLU est non-conjugé

Application: Western Blotting (WB)

Détail du produit anti-NAGLU anticorps

Épitope: C-Term

Séquence: LEALVDSVAQ GIPFQQHQFD KNVFQLEQAF VLSKQRYPSQ PRGDTVDLAK

Purification: Affinity purified

Immunogène: The immunogen is a synthetic peptide directed towards the C terminal region of human NAGLU

Information d'application

Indications d'application: Optimal working dilution should be determined by the investigator.

Restrictions: For Research Use only

Stockage

Format: Liquid

Buffer: Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.

Détails sur NAGLU

Antigène: NAGLU (N-Acetylglucosaminidase, alpha (NAGLU))

Autre désignation: NAGLU

Sujet: This gene encodes an enzyme that degrades heparan sulfate by hydrolysis of terminal N-acetyl-D-glucosamine residues in N-acetyl-alpha-D-glucosaminides. Defects in this gene are the cause of mucopolysaccharidosis type IIIB (MPS-IIIB), also known as Sanfilippo syndrome B. This disease is characterized by the lysosomal accumulation and urinary excretion of heparan sulfate.

Alias Symbols: NAG, MPS3B, UFHSD, MPS-IIIB

Protein Size: 639

ID gène: 4669

NCBI Accession: NM_000263, NP_000254

UniProt: P54802

Pathways: Glycosaminoglycan Metabolic Process