NAGLU anticorps (N-Term)

N° du produit ABIN5517087

Cet anticorps Lapin Polyclonal détecte spécifiquement NAGLU dans WB. Il présente une réactivité avec des échantillons de Humain, Boeuf (Vache), Chien et Porc.

Aperçu rapide pour NAGLU anticorps (N-Term) (ABIN5517087)

Antigène: NAGLU (N-Acetylglucosaminidase, alpha (NAGLU))

Reactivité: Humain, Boeuf (Vache), Chien, Porc

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp NAGLU est non-conjugé

Application: Western Blotting (WB)

Détail du produit anti-NAGLU anticorps

Épitope: N-Term

Fonction: NAGLU Antibody - N-terminal region

Séquence: GVLLLAGAGG AAGDEAREAA AVRALVARLL GPGPAADFSV SVERALAAKP

Homologie: Cow: 83%, Dog: 92%, Human: 100%, Pig: 79%

Attributs du produit: This is a rabbit polyclonal antibody against ANAG. It was validated on Western Blot.

Purification: Affinity purified

Immunogène: The immunogen is a synthetic peptide directed towards the N-terminal region of Human NAGLU

Information d'application

Indications d'application: Optimal working dilution should be determined by the investigator.

Commentaires:

We also sell a specific blocking peptide that can be used in combination with this antibody. You can find the blocking peptide under AAP58644-100UG

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 0.5 mg/mL

Buffer: Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Conseil sur la manipulation: prevent freeze-thaw cycles

Stock: 4 °C,-20 °C

Stockage commentaire: For short term use, store at 2-8C up to 1 week. For long term storage, store at -20 °C in small aliquots to prevent freeze-thaw cycles.

Détails sur NAGLU

Antigène: NAGLU (N-Acetylglucosaminidase, alpha (NAGLU))

Autre désignation: NAGLU

Sujet:

Background Information: This gene encodes an enzyme that degrades heparan sulfate by hydrolysis of terminal N-acetyl-D-glucosamine residues in N-acetyl-alpha-D-glucosaminides. Defects in this gene are the cause of mucopolysaccharidosis type IIIB (MPS-IIIB), also known as Sanfilippo syndrome B. This disease is characterized by the lysosomal accumulation and urinary excretion of heparan sulfate.

Gene Name: N-acetylglucosaminidase, alpha

Alternative Symbols: NAG, CMT2V, MPS3B, UFHSD, MPS-IIIB

Protein Name: Alpha-N-acetylglucosaminidase

Poids moléculaire: 81kDa

ID gène: 4669

NCBI Accession: NP_000254

UniProt: P54802

Pathways: Glycosaminoglycan Metabolic Process