GSS
Reactivité: Humain, Souris, Rat
WB, IHC, IF, IC
Hôte: Lapin
Polyclonal
unconjugated
Restrictions
For Research Use only
Format
Liquid
Concentration
1 mg/mL
Stock
4 °C,-20 °C,-80 °C
Stockage commentaire
Can be stored at +2°C to +8°C for 1 week. For long term storage, aliquot and store at -20°C to -80°C. Avoid repeated freezing and thawing cycles.
Antigène
Glutathione Synthetase (GSS)
Autre désignation
Glutathione Synthetase/GSS
Sujet
Glutathione synthetase, also known GSS, is the second enzyme in the glutathione biosynthesis pathway. It catalyses the condensation of gamma-glutamylcysteine and glycine, to form glutathione. Defects in GSS are the cause of glutathione synthetase deficiency (GSS deficiency) , also known as 5-oxoprolinuria or pyroglutamic aciduria. It is a severe form characterized by an increased rate of hemolysis and defective function of the central nervous system.