CLCN1 anticorps (AA 779-988)

N° du produit ABIN6138661

Détail du produit anti-CLCN1 anticorps

Antigène: CLCN1 (Chloride Channel 1, Skeletal Muscle (CLCN1))

Épitope: AA 779-988

Reactivité: Humain

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp CLCN1 est non-conjugé

Application: Western Blotting (WB), Immunohistochemistry (IHC)

Séquence: ARPTKKKTTQ DSTDLVDNMS PEEIEAWEQE QLSQPVCFDS CCIDQSPFQL VEQTTLHKTH TLFSLLGLHL AYVTSMGKLR GVLALEELQK AIEGHTKSGV QLRPPLASFR NTTSTRKSTG APPSSAENWN LPEDRPGATG TGDVIAASPE TPVPSPSPEP PLSLAPGKVE GELEELELVE SPGLEEELAD ILQGPSLRST DEEDEDELIL

Réactivité croisée: Humain, Souris, Rat

Attributs du produit: Polyclonal Antibodies

Purification: Affinity purification

Immunogène: Recombinant fusion protein containing a sequence corresponding to amino acids 779-988 of human CLCN1 (NP_000074.2).

Isotype: IgG

Information d'application

Indications d'application: WB,1:500 - 1:2000,IHC,1:50 - 1:200

Commentaires:

HIGH QUALITY

Restrictions: For Research Use only

Stockage

Format: Liquid

Buffer: PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Store at -20°C. Avoid freeze / thaw cycles.

Détails sur CLCN1

Antigène: CLCN1 (Chloride Channel 1, Skeletal Muscle (CLCN1))

Autre désignation: CLCN1 (CLCN1 Produits)

Synonymes: anticorps CLCN1, anticorps si:dkey-14o18.5, anticorps Clc-1, anticorps Clc1, anticorps SMCC1, anticorps adr, anticorps mto, anticorps myotonia, anticorps nmf355, anticorps SMCC, anticorps CLC1, anticorps chloride voltage-gated channel 1, anticorps chloride channel, voltage-sensitive 1a, anticorps chloride channel protein 1, anticorps chloride channel, voltage-sensitive 1, anticorps CLCN1, anticorps clcn1a, anticorps LOC100550479, anticorps LOC703944, anticorps Clcn1

Sujet: The CLCN family of voltage-dependent chloride channel genes comprises nine members (CLCN1-7, Ka and Kb) which demonstrate quite diverse functional characteristics while sharing significant sequence homology. The protein encoded by this gene regulates the electric excitability of the skeletal muscle membrane. Mutations in this gene cause two forms of inherited human muscle disorders: recessive generalized myotonia congenita (Becker) and dominant myotonia (Thomsen). Alternative splicing results in multiple transcript variants.,CLCN1,CLC1,Signal Transduction,Endocrine & Metabolism,Neuroscience,CLCN1

Poids moléculaire: 108 kDa

ID gène: 1180

UniProt: P35523