CLCN1 anticorps
Aperçu rapide pour CLCN1 anticorps (ABIN7227934)
Antigène
Voir toutes CLCN1 AnticorpsReactivité
Hôte
Clonalité
Conjugué
Application
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Fonction
- Rabbit Anti-CLCN1 Polyclonal Antibody
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Specificité
- The antibody detects endogenous levels of CLCN1 protein
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Purification
- The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
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Immunogène
- Synthesized peptide derived from part region of human CLCN1 protein
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Isotype
- IgG
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Indications d'application
- Optimal working dilutions should be determined experimentally by the investigator. Suggested starting dilutions are as follows: WB 1:500-2000,ELISA 1:5000-20000
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Restrictions
- For Research Use only
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Format
- Liquid
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Concentration
- 1 mg/mL
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Buffer
- PBS, 50 % glycerol, 0.05 % Proclin 300, 0.05 %BSA
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Agent conservateur
- ProClin
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Précaution d'utilisation
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Stock
- -20 °C
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Stockage commentaire
- Stable for one year at -20°C from date of shipment. For maximum recovery of product, centrifuge the original vial after thawing and prior to removing the cap. Aliquot to avoid repeated freezing and thawing.
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Date de péremption
- 12 months
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- CLCN1 (Chloride Channel 1, Skeletal Muscle (CLCN1))
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Autre désignation
- CLCN1
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Sujet
- Chloride channel protein 1, ClC-1, Chloride channel protein, skeletal muscleCLCN1 (Chloride Voltage-Gated Channel 1) is a Protein Coding gene. Diseases associated with CLCN1 include Myotonia Congenita, Recessive and Myotonia Congenita, Dominant The protein encoded by CLCN1 regulates the electric excitability of the skeletal muscle membrane. Mutations in CLCN1 cause two forms of inherited human muscle disorders: recessive generalized myotonia congenita (Becker) and dominant myotonia (Thomsen). Alternative splicing results in multiple transcript variants.
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Poids moléculaire
- 108kD
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ID gène
- 1180
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UniProt
- P35523
Antigène
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