GBA anticorps

N° du produit ABIN7248746

Détail du produit anti-GBA anticorps

Antigène: GBA (Glucosidase, Beta, Acid (GBA))

Reactivité: Humain, Souris

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp GBA est non-conjugé

Application: Western Blotting (WB), Immunohistochemistry (IHC), ELISA

Attributs du produit: Polyclonal Antibody

Purification: Antigen affinity purification

Immunogène: Synthetic peptide of human GBA

Isotype: IgG

Information d'application

Indications d'application: WB 1:500-1:2000, IHC 1:50-1:100, ELISA 1:5000-1:10000

Restrictions: For Research Use only

Stockage

Format: Liquid

Concentration: 1.56 mg/mL

Buffer: PBS with 0.05 % Sodium azide and 40 % Glycerol, pH 7.4

Agent conservateur: Sodium azide

Précaution d'utilisation: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Stock: -20 °C

Stockage commentaire: Store at -20°C. Avoid freeze / thaw cycles.

Détails sur GBA

Antigène: GBA (Glucosidase, Beta, Acid (GBA))

Autre désignation: GBA (GBA Produits)

Synonymes: anticorps GBA1, anticorps GCB, anticorps GLUC, anticorps BETA-GLUCOSIDASE, anticorps T12J13.8, anticorps T12J13_8, anticorps beta glucosidase 25, anticorps PSPTO3318, anticorps PSPTO4290, anticorps GC, anticorps GCase, anticorps betaGC, anticorps glucosylceramidase beta, anticorps beta glucosidase 25, anticorps beta-glucosidase, anticorps Beta-glucosidase, anticorps glucosidase, beta, acid, anticorps glucosylceramidase, anticorps bglX-2, anticorps GBA, anticorps BGLU25, anticorps PSPTO_3318, anticorps bglX, anticorps bglA4, anticorps Gba, anticorps LOC100399524, anticorps bglA.2, anticorps bglX-2

Sujet: This gene encodes a lysosomal membrane protein that cleaves the beta-glucosidic linkage of glycosylceramide, an intermediate in glycolipid metabolism. Mutations in this gene cause Gaucher disease, a lysosomal storage disease characterized by an accumulation of glucocerebrosides. A related pseudogene is approximately 12 kb downstream of this gene on chromosome 1. Alternative splicing results in multiple transcript variants.

Poids moléculaire:

Observed_MW: Refer to figures

Calculated_MW: 60 kDa

UniProt: P04062

Pathways: Cellular Glucan Metabolic Process